Pediatrik Göğüs Deformitelerinin Klinik, Demografik ve Ekokardiyografik Özellikleri

Amaç: Çocuk kardiyoloji kliniğinde göğüs deformitesi tanısı alan çocukların klinik, demografik, klinik ve ekokardiyografik bulgularını retrospektif olarak değerlendirmeyi amaçladık. Gereç Ve Yöntem: Bu çalışmaya altı yıl boyunca (Ocak 2017-Aralık 2022) pediatrik kardiyoloji birimimize göğüs deformitesi ile başvuran 18 yaş altı çocuklar dahil edildi. Bulgular: Hastaların yaş ortalaması 9,9 ± 5,2 median:11 yaş (0-18 yaş) idi. Anormal ekokardiyografik bulguları olan 89 hasta: 42 (%9,56) mitral kapak prolapsusu, 18 (%4,1) atriyal septal defekt, 9 (%2) ventriküler septal defekt, 8 (%1,82) aort kapak darlığı olmayan biküspid aort kapak, 5 (%1,1) patent duktus arteriozus, 2 (%0,45) pulmoner darlık, 2 (%0,45) büyük arter transpozisyonu, 2 (%0,45) hipertrofik kardiyomiyopati, subaortik ridge 1 (%0,27) idi. Pektus ekskavatumlu olguların %13.4'ünde kardiyak bası vardı. 13(%3) hasta göğüs cerrahisi tarafından opere edildi. Göğüs deformitesi ile kliniğimize başvuran 7 hastada Marfan Sendromu, 2 hastada Noonan Sendromu teşhis edildi. Sonuç: Göğüs deformitesi olan hastalarda ekokardiyografik incelemenin doğumsal kalp hastalıklarının tanısında, kalp sıkışması bulgusunun erken tanı ve tedavisinde önemli olduğunu düşünüyoruz.

Anahtar Kelimeler:

çocuklar, göğüs deformitesi, ekokardiyografi

Clinical, Demographic and Echocardiographic Characteristics Of Pediatric Chest Deformities

Objective: We aimed to retrospectively evaluate the clinical, demographic, clinical and echocardiographic findings of children diagnosed with chest deformity in the pediatric cardiology clinic. Material and Method: This study enrolled children under the age of 18 years who were referred with chest deformity to our pediatric cardiology unit, over a period of six years (January 2017-December 2022). Results: The mean age of the patients was 9.9 ± 5.2 years, median 11 years (0-18 years old). 89 patients with abnormal echocardiographic findings: 42 (9.56%) mitral valve prolapse, 18 (4.1%) atrial septal defect, 9 (2%) ventricular septal defect, 8 (1.82%) bicuspid without aortic valve stenosis aortic valve, 5 (1.1%) patent ductus arteriosus, 2 (0.45%) pulmonary stenosis, 2 (0.45%) great artery transposition, 2 (0.45%) hypertrophic cardiomyopathy, subaortic ridge 1 (% 0.27). Cardiac compression was present in 13.4% of the cases with pectus excavatum. 13(%3) patients were operated by a thoracic surgeon. Marfan Syndrome was diagnosed in 7 patients and Noonan Syndrome was diagnosed in 2 patients who applied to our clinic with chest deformity. Conclusion: We suggest that echocardiographic examination in patients with chest deformity is important in the diagnosis of congenital heart diseases, early diagnosis and treatment of heart compression finding.

Keywords:

children, chest deformity, echocardiography,

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