Gülsen KESKİN, Mine AKIN, Sibel SAYDAM, Sengül ÖZMERT, Yeşim ŞENAYLI, Feyza SEVER, Devrim Tanıl KURT

17 Yaşında Kız Hastada Feokromasitoma Eksizyonu İçin Uygulanan Anestezi Yönetimi: Olgu Sunumu

Kromafin dokularının nadir bir tümörü olan feokromasitoma yüksek miktarda katekolamin salgılanmasıyla karakterizedir. Bu tümörlerin sadece %5’i çocuk populasyonunda tanımlanmıştır. Bu makalede feokromasitomanın yanında Ailesel Akdeniz Ateşi (FMF) de bulunan 17 yaşındaki kız hastanın sağ sürrenal kitlesinin eksizyonu için uygulanan anestezi yönetimi sunuldu. Hastanın preoperatif kan basıncı kontrolü fenoksibenzamin ile sağlandı. Genel anestezi uygulaması için tiyopental, vekuronyum, fentanil and sevofluran tercih edildi. Peroperatif kan basıncı kontrolünde sodyum nitroprussid ve fentolamin kullanıldı. Postoperatif ağrı kontrolü tramadol ve diklofenak ile sağlandı. Hasta iyi bir preoperatif hazırlık ve peroperatif yönetimle sorunsuz tedavi sürecinin ardından taburcu edildi.

Anahtar Kelimeler:

Anestezi, Çocuk, Feokromasitoma

Anesthesia Management for Pheochromocytoma Removal in a 17-Year-Old Girl: Case Report

A rare tumor of the chromaffin tissue, pheochromocytoma is characterized by increased secretion of catecholamines. Pediatric cases represent only 5% of all pheochromocytomas. In this report, we presented anesthesia management of a 17-year-old girl who would undergo right suprarenal mass excision due to pheochromocytoma accompanied with familial Mediterranean fever (FMF). Preoperative blood pressure control was achieved with phenoxybenzamine. General anesthesia was established with thiopental, vecuronium, fentanyl, and sevoflurane. Sodium nitroprusside and phentolamine was used for perioperative blood pressure control. Tramadol and diclofenac were administered for postoperative pain. The patient was discharged after a good preoperative preparation and perioperative management with uneventful treatment period.

Keywords:

Anesthesia, Child, Pheochromocytoma,

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