Uğur ERSOY, M. Fatih AKDOĞAN, Fatih PALİT, Haluk ŞAVLI, Hasan MAĞIN, Murat GÜCÜN, At ALL.

İKİ VAKA NEDENİYLE TROMBOTİK TROMBOSİTOPENİK PURPURA

Trombotik Trombositopenik Purpura (TTP) ; Ateş, akut böbrek yetmezliği, nörolojik bozukluklar, trombositopeni ve mikroanjiopatik hemolitik anemi ile seyreden bir sendromdur. Nadir görülen bu hastalık (4-11/1.000.000), klinik olarak dissemine intravasküler koagulasyon (DİK), hemolitik üremik sendrom (HÜS) ve Evans sendromu gibi anemi yapan diğer nedenlerle karışabilir. İki vaka nedeniyle, TTP güncel literatür ışığında tekrar gözden geçirilmiştir.

Anahtar Kelimeler:

Trombositopeni, Purpura, Plazmaferez

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