Necmettin AKDENİZ, Ömer Faruk ELMAS, Okan KIZILYEL, Mahmut Sami METİN, Betül GÜNDOĞDU

Telengiectasia macularis eruptiva perstans: A case report

Kutanöz mastositozlar, deride mast hücre infiltrasyonu ile karakterize hastalık grubudur. Deri lezyonlarına iç organ tutulumu da eşlik edebilir.Telenjiektazia makülaris erüptiva perstans, kutanöz mastositozların nadir bir formudur ve genellikle erişkinlerde görülür. Sıklıkla gövdedeyuvarlak, oval, kahverengi kırmızı maküler lezyonlar görülür. Olguların üçte birinde sistemik tutulum olabilir. Tedavi, hastalarda sistemiktutulum ve klinik bulguların varlığına göre değişir. 39 yaşındaki erkek hasta gövde ve kollarda yaygın, kahverengi, kaşıntılı makülerlezyonlarla başvurdu. Klinik ve histopatolojik olarak telenjiektazia makülaris erüptiva perstans tanısı konan hastada sistemik tutulumsaptanmadı. Telenjiektazia makülaris erüptiva perstans kutanöz mastositozun atipik bir formu olması ve nadir görülmesi nedeniyle olgumuzusunmayı uygun gördük.

Telenjiektazia makülaris erüptiva perstans: Bir olgu sunumu

Cutaneous mastocytosis is a group of diseases characterized by infiltration of mast cells in the skin. Telengiectasia macularis eruptivaperstans is a rare form of cutaneous mastocytosis and it is usually seen in adults. Round, oval, brown-red macular lesions are usually seen onthe trunk. Systemic involvement may be observed in one third of the patients. Treatment depends on the presence of systemic involvementand clinical symptoms of patients. Our patient was a 39 years old man presented with widespread brownish pruritic macular lesions on histrunk and arms. There was no systemic involvement. The patient was diagnosed with telengiectasia macularis eruptiva perstans bothclinically and histopathologically. We decided to report this case because telengiectasia macularis eruptiva perstans is an atypical form ofcutaneous mastocytosis and is rarely seen.

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