Aytekin GÜVEN

Apical hypertrophic cardiomyopathy mimics acute coronary syndrome: Case report

Apikal hipertrofik kardiyomiyopati (HKM) hipertrofik kardiyomiyopatinin nispeten nadir görülen, özellikle sol ventrikülün apeksinin miyokardının hipertrofisini içeren bir tipidir. İlk olarak Sakamoto ve Yamaguchi tarafından açıklanan apikal HKM’nin tipik bulguları, elektrokardiografide dev T dalga negatifliği ve sol ventrikülografide diyastole sonunda sol ventrikül kavitesinin “maça ası” görünümüdür. Apikal HKM diğer HKM ile karşılaştırıldığında genellikle iyi seyirlidir. Apikal tip HKM’nin en iyi tanı aracı transtorasik ekokardiyografi (TTE) olmasına rağmen rutin işlemlerde nadiren gözden kaçabilir. Bu olgu sunumunda, başka bir merkeze akut koroner sendrom tablosunda başvuran ve rutin TTE incelemede HKM’si gözden kaçan fakat gerçekte HKM’li 38 yaşında erkek hastadan bahsedilmektedir.

Akut koroner sendromu taklit eden apikal hipertrofik kardiyomiyopati: Olgu sunumu

Apical hypertrophic cardiomyopathy (HCM) is a relatively rare form of HCM, in which the hypertrophy of myocardium predominantly involves the apex of the left ventricle. The typical features of Apical HCM, first described by Sakamoto and Yamaguchi and their associates, consist of giant T wave negativity in the electrocardiogram and a “spadelike” configuration of the LV cavity at end-diastole on left ventriculography. Apical HCM generally has a more benign course compared to other variants HCM.Although the best tool for diagnosis of HCM is transthoracic echocardiography (TTE) apical type of HCM may be occasionally overlooked during routine examination. We present a 38 years old male with HCM who was referred from the out center with the preliminary diagnosis of acute coronary syndrome but indeed he had HCM and in whom HCM was overlooked during TTE examination.

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