620254

WILLIAMS BEUREN SYNDROME, A SHORT COMMUNICATION OF A PECULIAR CASE

Williams-Beuren syndrome (WBS) is a rare congenital disorder that includes cardiovascular problems, mental retardation, distinctive facial features and dental anomalies. This case report the treatment of a tooth fracture after dental trauma in a 13-year-old male with WBS syndrome. Intraoral clinical examination revealed anterior interdental space and enamel hypoplasia in incisors. Dental treatment included: The fracture tooth fragment was restored after basic behavioral orientation

Keywords:

Williams-Beuren syndrome, tooth fracture tooth anomalies,

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