Mustafa REŞORLU, Canan AKGÜN TOPRAK, Muhsin Özgün ÖZTÜRK

Periaortitli Hastada Retroperitoneal ve Mediastinal Fibrozis Birlikteliği: Olgu Sunusu

Kronik periaortit daha sık orta yaş erkekleri etkilemekte ve nadir olarak görülmektedir. Patofizyolojisinde otoimmünitenin etkili olduğu ve idiopatik retroperitoneal fibrozis, perianevrizmal fibrozis, enflamatuar abdominal aort anevrizması ile ilişkili olduğu ileri sürülmektedir. Retroperitoneal fibrozis olgularının büyük kısmı idiopatiktir. Mediastinal fibrozis ise sıklıkla enfeksiyoz süreçle ilişkilidir. Bu iki patolojik tablonun birlikteliği ise oldukça nadirdir. Biz bu çalışmamızda periaortiti olan bir hastamızda eşlik eden retroperitoneal ve mediastinal fibrozis birlikteliğini sunmayı amaçladık

Anahtar Kelimeler:

Retroperitoneal fibrozis, mediastinal fibrozis, periaortit

Comorbid Retroperitoneal and Mediastinal Fibrosis in a Case of Periaortitis

Chronic periaortitis is a rare condition. Middle-aged males comprise a large proportion of patients. An association has been proposed with idiopathic retroperitoneal fibrosis, perianeurysmal fibrosis and inflammatory abdominal aortic aneurysm, and autoimmunity has been implicated in the pathophysiology. Comorbidity of retroperitoneal fibrosis, which is frequently idiopathic, and mediastinal fibrosis, which is particularly associated with infectious processes, is rare. The purpose of this study was to report a case of comorbid retroperitoneal and mediastinal fibrosis in a patient with periaortitis, together with imaging findings

Keywords:

Retroperitoneal fibrosis, Mediastinal fibrosis, Periaortitis,

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