Göğüs Duvarı Deformitesi Olan Çocukların Demografik, Klinik ve Ekokardiyografik Özellikleri

GİRİŞ ve AMAÇ: Göğüs duvarı deformitesi olan çocukların demografik, klinik ve ekokardiyografik özelliklerinin değerlendirilmesi amaçlandı. YÖNTEM ve GEREÇLER: Çocuk kardiyoloji ünitesinde üç yıl süreyle göğüs duvarı deformitesi tanısı alan hastalar retrospektif olarak değerlendirildi. BULGULAR: Ortanca yaşı 8 olan hastaların ortalama yaşı 7.6 ± 4.5 idi. Göğüs duvarı deformitesi olan yüz altmış dört (% 80) hastanın ekokardiyografik değerlendirmesi normaldi. Ekokardiyografik tanıları 10 (% 4.87) atriyal septal defekt, 8 (% 3.90) mitral kapak prolapsusu, 7 (% 3.41) hafif mitral yetersizliği, 5 (% 2.44) darlık olmayan biküspit aort kapağı, 4 (% 1.95) ventriküler septal defekt, 2 (% 0.98) hafif aort kapak yetersizliği, 2 (% 0.98) dekstrokardi, 2 (% 0.98) aort koarktasyonu ve 1 (% 0.49) kompleks kalp defekti (pulmoner atrezi ve ventriküler septal defekt) idi. Ekokardiyografi ile değerlendirilen sağ kalbe bası bulgusu 15 (% 7.3) hastada saptandı. TARTIŞMA ve SONUÇ: Göğüs duvarı deformitelerinin doğuştan kalp hastalıkları ile ilişkili olması ve kalbe bası bulgusu oluşturabilmeleri sebebiyle ekokardiyografi ile değerlendirilmesi defektlerin en uygun şekilde yönetilmesini sağlayacaktır.ABSTRACT INTRODUCTION: To determine the demographic, clinical and echocardiographic characteristics of children with chest wall deformities. METHODS: The patients diagnosed with chest wall deformities were investigated retrospectively in the pediatric cardiology unit over a period of three years. The study enrolled 205 children under the age of 18 years diagnosed with chest wall deformities. RESULTS: The mean age of the patients was 7.6 ± 4.5 years with a median of 8 years. One hundred and sixty four (80 %) patients with chest wall deformities were found to have normal echocardiography results. Incidental echocardiographic diagnoses included 10 (4.87%) atrial septal defects, 8 (3.90%) mitral valve prolapses, 7 (3.41%) mild mitral regurgitations, 5 (2.44%) bicuspid aortic valve without aortic valve stenoses, 4 (1.95%) ventricular septal defects, 2 (0.98%) mild aortic regurgitations, 2 (0.98%) dextrocardia, 2 (0.98%) coarctations of the aorta, and  1 (0.49%) complex cardiac defect (pulmonary atresia and VSD). Compression in the right heart was evaluated by echocardiography in 15 patients (7.3%). DISCUSSION AND CONCLUSION: Because chest wall deformities are associated with congenital heart defects in children and may cause compression in the right heart, evaluation by echocardiography can ensure an optimal management of the defects.

Demographic, Clinical and Echocardiographic Characteristics of Children with Chest Wall Deformities Göğüs Duvarı Deformitesi Olan Çocukların Demografik, Klinik ve Ekokardiyografik Özellikleri

INTRODUCTION: To determine the demographic, clinical and echocardiographic characteristics of children with chest wall deformities. METHODS: The patients diagnosed with chest wall deformities were investigated retrospectively in the pediatric cardiology unit over a period of three years. The study enrolled 205 children under the age of 18 years diagnosed with chest wall deformities. RESULTS: The mean age of the patients was 7.6 ± 4.5 years with a median of 8 years. One hundred and sixty four (80 %) patients with chest wall deformities were found to have normal echocardiography results. Incidental echocardiographic diagnoses included 10 (4.87%) atrial septal defects, 8 (3.90%) mitral valve prolapses, 7 (3.41%) mild mitral regurgitations, 5 (2.44%) bicuspid aortic valve without aortic valve stenoses, 4 (1.95%) ventricular septal defects, 2 (0.98%) mild aortic regurgitations, 2 (0.98%) dextrocardia, 2 (0.98%) coarctations of the aorta, and  1 (0.49%) complex cardiac defect (pulmonary atresia and VSD). Compression in the right heart was evaluated by echocardiography in 15 patients (7.3%). DISCUSSION AND CONCLUSION: Because chest wall deformities are associated with congenital heart defects in children and may cause compression in the right heart, evaluation by echocardiography can ensure an optimal management of the defects.

___

  • 1. Fokin AA, Steuerwald NM, Ahrens WA, Allen KE. Anatomical, histologic, and genetic characteristics of congenital chest wall deformities. Semin Thorac Cardiovasc Surg 2009;21:44-57.
  • 2. Brochhausena C, Salmai T, Müllera FKP, Schmitta VH, Coerdta W, Wihlmc JM, Schierb F, Kirkpatricka CJ. Pectus excavatum: history, hypotheses and treatment options. Interactive CardioVascular and Thoracic Surgery 2012;14: 801–6.
  • 3. Park JM, Varma SK. Pectus excavatum in children : Diagnostic significance for mitral valve prolapse. The Indian Journal of Pediatrics 1990;57 219-22. 4. Tang M, Nielsen HH, Lesbo M, Frøkiær J, Maagaard M, Pilegaard HK, Hjortdal VE. Improved cardiopulmonary exercise function after modified Nuss operation for pectus excavatum. Eur J Cardiothorac Surg 2012;41:1063-7.
  • 5. Desmarais TJ, Keller MS. Pectus carinatum. Curr Opin Pediatr 2013;25:375-81.
  • 6. Shamberger RC, Welch KJ, Castaneda AR, Keane JF, Fyler DC. Anterior chest wall deformities and congenital heart disease. J Thorac Cardiovasc Surg 1988:96(3):427-32.
  • 7. Simsek Z, Gunay E, Aksakal E, Kutucularoglu MG, Guneren G. İzole pektus ekskavatumlu genç erişkin hastaların kardiyopulmoner bulgularının değerlendirilmesi. Anadolu Kardiyol Derg 2011;1:77-8.
  • 8. Akcali Y, Ceyran H, Hasdiraz L. Chest wall deformities. Acta Chir Hung 1999; 38:1-3.
  • 9. Esme H, Bukulmez A, Dogru O, Solak O. Afyon ili ilköğretim okulu çocuklarında gögüs duvarı deformitelerinin prevalansı. Turkish J Thorac Cardiovasc Surg 2006;14:34-7.
  • 10. Randhawa AK, Mishra C, Gogineni SB, Shetty S. Marfan syndrome: report of two cases with review of literature. Niger J Clin Pract 2012;15:364-8.
  • 11. Kikuchi S, Ingu A, Ito M. Simultaneous repair of pectus excavatum and tetralogy of fallot: report of a case. Ann Thorac Cardiovasc Surg 2005;11:320-3.
  • 12. Coln E, Carrasco J, Coln D. Demonstrating relief of cardiac compression with the Nuss minimally invasive repair for pectus excavatum. J Pediatr Surg 2006;41:683-6.
  • 13. Guntheroth WG, Spiers PS. Cardiac function before and after surgery for pectus excavatum. Am J Cardiol 2007;12:1762-4.
Güncel Pediatri-Cover
  • Başlangıç: 2003
  • Yayıncı: Erkan Mor
Sayıdaki Diğer Makaleler

Karbonmonoksit zehirlenmelerinde karboksihemoglobin düzeyleri önemsenmelidir Carboxyhemoglobin levels should be considered important on carbonmonoxide poisoning

Ali YURTSEVEN, Eylem Ulaş SAZ

Çocuk Yoğun Bakım Ünitesine Yatan Hastaların Değerlendirilmesi Evaluation Of The Patients Admitted To The Pediatric Intensive Care Unit

Lütfiye Nilüfer YEĞİN, Yasemin SANCAK, Çiğdem AŞUT, Zeynep GİZEM, Ergün ÖZDEL

Anne Sütü, Anne Sütü ile Birlikte Mama ve Sadece Mama ile Beslenen Bebeklerin Koklear Fonksiyonlarının Değerlendirilmesi

Mesut KAYA, Selim ÜNSAL, Ahmet Yasin SARIGÜL, Çiğdem Nüket YÜKSEL

Juguler Kateter Komplikasyonu Olarak Hematomun Neden Olduğu Vazovagal Bradikardi

Oğuzhan BABACAN, Erman ATAŞ, Nadir KORKMAZER, Vural KESİK

Geç tanı alan konjenital hipotiroidli bir çocukta L-tiroksin tedavisi sonrası saç dökülmesi Hair loss after treatment with L-thyroxine in a child with a delayed diagnosis of congenital hypothyroidism

Ayşegül YALÇINKAYA İYİDAL, Fatma Arzu KILIÇ

Adölesan Dönemi Beslenme ve Sorunları Nutrition and Issues in Adolescence Period

Sabiha Zeynep AYDENK KÖSEOĞLU, Aslı ÇELEBİ TAYFUR

Önemli Bir Halk Sağlığı Problemi: Vitamin B12 Eksikliği An important public health problem: Vitamin B12 deficiency

Şahin ERDÖL

Göğüs Duvarı Deformitesi Olan Çocukların Demografik, Klinik ve Ekokardiyografik Özellikleri

Eyüp ASLAN, Ahmet SERT, Fatih SAP, Ebru AYPAR, Dursun ODABAŞ

Çocuk ve Adölesanlarin Elektronik Medya Kullanımının Obezite ve Uyku Sorunlarına Etkisi The Effect of Electronic Media Use Children and Adolescents with Obesity and Sleep

Duygu AKÇAY

Büyüme Hormon Tedavisi Kemik Yaşını İlerletir mi? Does Growth Hormone Treatment Advance Bone Age?

Enes SALI, Halil SAĞLAM, Erdal EREN, Ömer TARIM