Zerrin Özçelik, Okan Dilek, Ali Orgun, Orkun Tolunay, Aylin Kont Özhan

Konjenital lober amfizem: olgu sunumu

Konjenital lober amfizem, alt solunum yollarında hiperinflasyon ile karakterize nadir rastlanan akciğerin doğumsal bir anomalisidir. Konjenital lober amfizemli hastalarda klinik seyir, hastalığın ortaya çıktığı yaşa, etkilenen loba veya normal lobların baskılanmasına bağlı olarak değişebilir. Tanısı klinik ve görüntüleme yöntemleri ile birlikte konulur. Semptomları hafif olan olgular konservatif tedavi ile izlenirken, ağır solunum semptomu olan olguların lobektomi ile tedavisi iyi sonuçlar vermektedir. Konjenital lober amfizem, nadir görülen bir akciğer anomalisi olmasına rağmen, nedeni bilinmeyen solunum sıkıntısı olan hastalarda ayırıcı tanıda göz önünde bulundurulması gereken bir hastalıktır. Bu yazıda erken dönemde konjenial lober amfizem tanısı konulan, hafif semptomları olması nedeniyle de konservatif tedavi yöntemleri ile izlenilen 4 aylık kız hasta sunulmaktadır.

Anahtar Kelimeler:

çocuk, konjenital lober amfizem, konservatif tedavi

Congenital lobar emphysema: a case report

Congenital lobar emphysema is a rare congenital anomaly of the lung characterized by hyperinflation of the lower respiratory tract. In patients with congenital lobar emphysema, the clinical course may vary depending on the age at which the disease occurs, suppression of the affected lobe or normal lobes. Diagnosis is made together with clinical and imaging methods. While the patients with mild symptoms are followed with conservative treatment, the treatment of patients with severe respiratory symptoms with lobectomy gives good results. Although congenital lobar emphysema is a rare lung anomaly, it should be considered in the differential diagnosis in patients with unresolved respiratory distress. In this article, we present a 4-month-old girl who was diagnosed with congenial lobar emphysema in the early period and who was followed with conservative treatment because of mild symptoms

Keywords:

child, congenital lobar emphysema, conservative treatment,

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