Mehmet CANPOLAT, Hatice Gamze POYRAZOĞLU, Sefer KUMANDAŞ, Hüseyin PER, Hakan GÜMÜŞ, Ali YIKILMAZ, Pembe SOYLU

Dyke-Davidoff-Masson sendromu olgusu

Dyke-Davidof-Masson sendromu, konvülsiyon, fasiyal asimetri, kontrolateral hemipleji veya hemiparezi, mental retardasyon ile karakterize bir sendromdur. Klinik bulgular, beyin zedelenmesinin düzeyine bağlı olarak değişiklikler gösterebilir. Serebral hemiatrofi ile ilişkili olarak hemipleji, konvülsiyon, öğrenme güçlüğü ve epilepsi görülebilir. On yaşında konvülsiyon ile başvuran, fizik muayenede sol hemiparezi ve manyetik rezonans görüntülemede serebral hemiatrofisi tespit edilen Dyke-Davidoff-Masson sendromlu bir erkek çocuk sunulmuştur.

A case of Dyke-Davidoff-Masson syndrome

Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis and mental retardation. The clinical findings may be of variable degree according to the extent of brain injury. Cerebral hemiatrophy is frequently associated with hemiplegia, convulsions, mental deficit and subsequent epilepsy. In this article, a case of a ten-year-old boy with Dyke-Davidoff-Masson syndrome characterized by cerebral hemiatrophy in magnetic resonance imaging, left hemiparesis in physical examination and presence of seizures is presented.

PDF

___

1. Dyke CG, Davidoff LM, Masson CB. Cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Surg Gynecol Obstet 1933;57:588-600.
2. Solomon GE, Hilal SK, Gold AP, Carter S. Natural history of acute hemiplegia of childhood. Brain 1970;93(1):107-20.
3. Sener RN, Jinkins JR. MR of craniocerebral hemiatrophy. Clin Imaging 1992;16(2):93-7.
4. Tasdemir HA, Incesu L, Yazicioglu AK, Belet U, Güngör L. Dyke-Davidoff-Masson syndrome. Clin Imaging 2002;26(1):13- 7.
5. Pendse NA, Bapna P, Menghani V, Diwan A. Dyke-Davidoff- Masson syndrome (DDMS). Indian J Pediatr 2004;71(10):943.
6. Aguiar PH, Liu CW, Leitão H, Issa F, Lepski G, Figueiredo EG, et al. MR and CT imaging in the Dyke-Davidoff-Masson syndrome. Report of three cases and contribution to pathogenesis and differential diagnosis. Arq Neurosiquiatr 1998;56(4):803-7.
7. Garg RK, Karak B. Cerebral hemiatrophy: a possible etiological relation with febrile seizures. Indian Pediatr 1998;35(1):79-81.
8. Unal O, Tombul T, Cirak B, Anlar O, Incesu L, Kayan M. Left hemisphere and male sex dominance of cerebral hemiatrophy (Dyke-Davidoff-Masson Syndrome). Clin Imaging 2004;28(3):163-5.
9. Alkan A, Baysal T, Kıroğlu Y, Sığırcı A, Orkan İ. Dyke- Davidoff-Masson sendromunda MRG bulguları. İnönü Üniversitesi Tıp Fakültesi Derg 2001;8(1):37-40.
10. Sener RN. Growing skull fracture in a patient with cerebral hemiatrophy. Pediatr Radiol 1995;25(1):64-5.
11. Kesken S, Ersoy E, Özkan M, Zorlu Y. Dyke-Davidoff sendromu iki olgu sunumu. Türk Nöroloji Derg 1995;4:236-8.
12. Wheless JW, Clarke DF, Arzimanoglou A, Carpenter D. Treatment of pediatric epilepsy: European expert opinion, 2007. Epileptic Disord 2007;9(4):353-412.