Aylar POYRAZ, Ömer ULUOĞLU, Arzu OKUR, Serdar KULA, Rana OLGUNTÜRK, Aynur OGUZ, Ceyda KARADENİZ, Faruk Guclu PİNARLİ

Mediastinal Hemangiopericytoma with Bone Metastases in a 2.5 Year-old-boy

Hemanjioperisitoma, kapiller perisitlerin proliferasyonu ile karakterize bir yumuşak doku sarkomudur. Burada, mediastinal bir kitle ve birden çok kemik metastazları olan 2,5 yaşında bir erkek olgu sunulmaktadır. Tümör çok agresif seyretmiş ve yoğun kemoterapiye ragmen ilerleme göstererek kötü bir prognoza yol açmıştır.

Kemik Metastazı olan Mediastinal Hemanjioperisitomalı 2.5 Yaşında Bir Erkek Olgu

Hemangiopericytoma (HPC) is a soft tissue sarcoma characterized by the proliferation of capillary pericytes. Here we present a 2.5 year-old-boy with a mediastinal mass and multiple bone metastases. The tumor was very aggressive and showed progression despite aggressive chemotherapy, leading to a dismal prognosis.

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