Ayşe DURSUN, Erdoğan İNAL, S. Sabri USLU, M. Hantürk ATİLLA, Ahmet KÖYBAŞIOĞLU, Fikret İLERİ

Chondrosarcoma of sphenoethmoid region: Report of a case

Kondrosarkom malign tümör olmasına karşın yavaş büyür ve geç metastaz yapar. Baş boyun bölgesinde özellikle paranazal sinüslerde çok az rastlanır. Etyolojisinde konfenital ve akkiz faktörler mevcuttur. Sfenoetmoid bölgeden köken alan kondrosarkomlar vital yapılara invazyon sonucu semptomlar oluşturur. Baş ağrısı ve görme bozukluğu en sık yol açtığı semptomlardır. Tanısında öncelikli olarak bilgisayarlı tomografi ve magnetik rezonans görüntüleme kullanılır. Tedavisi radikal cerrahi eksizyondur. Radyoterapi ve kemoterapi ancak radikal cerrahi eksizyonun yapılamadığı durumlarda ek tedavi olarak uygulanır. Bu çalışmada sfenoetmoid bölgeden köken alan kondrosarkom vakası sunulmuştur.

Sfenoetmoid bölge kondrosarkomu: Vaka sunumu

Chondrosarcoma is a malignant tumor that has a slow growth with late metastasis. It is rarely seen in the head and neck and even less frequently in the paranasal sinuses. Congenital and acquired factors are involved in etiology. Chondrosarcoma arising from the sphenoethmoid region gives rise to symptoms especially by invasion of vital structures. Headache and visual disturbances are the most common of these symptoms. Computed tomography (CT) and magnetic resonance imaging (MRI) aid in diagnosis. Treatment of chondrosarcoma is radical surgical excision but radiotherapy and chemotherapy are additional treatment modalites in selected cases. A case of chondrosarcoma of sphenoethmoid region is presented in this study.

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