Mehmet Nur KAYA, Ömer TOPRAK, Sultan TÜREL, Uğur ERGÜN, Taha Yasin ARSLAN

Congenital Extrahepatic Portosystemic Shunt: Abernethy Malformation Type 2

Abernethy malformation is a vascular congenital anomaly in which extrahepatic portocaval shunts develop. The patient was admitted to the gastroenterology department with complaints of abdominal pain and nausea. Ammonia and bilirubin levels wereincreased in the laboratory values and other liver function values were normal. The shunt was detected between the inferior venacava and portal vein by ultrasonography and computed tomography, and the portal vein was hypoplastic. In this case report, wepresent a male patient diagnosed with Abernethy malformation type 2.

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