Derya ÖZKAN, Osman Bulut OCAK, Hilal Zeynep CEYLAN, Birsen GÖKYİĞİT, Muhittin TAŞKAPILI

Millard-Gubler Sendromlu bir olguda şaşılık ve okuloplasti cerrahisi

Millard-Gubler Sendromu (MGS), 6. ve 7. kraniyal sinir periferik felcine eşlik eden vücut karşı tarafında hemiparezi ya da hemipleji ile seyreder. Etiyolojide yaşa göre değişkenlik görülmekle birlikte pons hasarı ön plandadır. Tedavi ve prognoz esas olarak etiyolojiye bağlıdır. Kliniğimize sağ gözde içe kayma şikayetiyle başvuran 18 yaşındaki erkek hastada Millard-Gubler Sendromu düşünülmüş, ancak etiyoloji belirlenememiştir. Hastaya şaşılık ve lagoftalmus nedeniyle operasyonlar uygulanmış, sonuç olarak ortofori sağlanmış ve lagoftalmus düzeltilmiştir. Hastalara nöroloji kliniğinin bilgisi dışında yapılacak cerrahi müdahalelerin, hastalığın oküler bulgularını maskeleyebileceği unutulmamalı, multidisipliner yaklaşımla, nörolojik rehabilitasyonu da içeren konservatif tedavi uygulanmalıdır.

Strabismus and oculoplastic surgery in a case with Millard-Gubler Syndrome

Millard-Gubler Syndrome (MGS) progresses with contralateral hemiparesis or hemiplegia accompanying peripheral palsies of 6th and 7th cranial nerves. Although the etiology varies according to age, pons damage is prominent. Treatment and prognosis mainly depend on etiology. An 18-year- old male patient applied to our clinic with the complaint of crossing in the right eye, Millard-Gubler Syndrome was considered but the etiology could not determine. Operations were performed to the patient due to strabismus and lagophthalmos, as a result orthophoria was provided and lagophthalmos was corrected. It should be kept in mind that may mask ocular findings of the disease if surgical interventions to be performed on patients without the knowledge of the neurology clinic, with a multidisciplinary approach, conservative treatment, including neurological rehabilitation should be administered.

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