Mücahit Gür, Leyla KUTLUCAN, Hayati KANDİŞ, Yasin TÜRKER, Leyla Yılmaz AYDIN, Süber DİKİCİ, Ertuğrul KAYA

ANİ KARDİYAK ARRESTLE BAŞVURAN KONJENİTAL UZUN QT SENDROMU

Uzun QT sendromu (LQTS); çarpıntı atakları, tekrarlayan senkop, konvulsiyonlar ve ani ölümeneden olabilen, ventriküler aritmilerle karakterize bir hastalıktır. Mortal seyredebilen aritmiler,ventriküler repolarizasyon fazındaki uzama sonucu oluşur ve bu uzamalar edinsel yadakonjenital olabilir. Bu yazıda ani kardiyak arrest ile takip edilip, implante edilebilenkardiyoverter defibrilatör (ICD) ile düzelme sağlanabilen, bir konjenital LQT sendromuna dikkatçekilmiştir

Anahtar Kelimeler:

Konjenital uzun QT sendromu, ani kardiyak arrest, implante edilebilenkardiyoverter defibrilatör

Congenital Long QT Syndrome Referred with Sudden Cardiac Arrest

The long QT syndrome (LQTS) is characterized with arrhythmic attacks, repeating syncopes,seizures, and ventricular arrhythmias leading to sudden death. Arrhythmias with a potential ofmortal course develop due to elongation of ventricular repolarization, either acquired or inborn.Herein the present paper, a case of congenital LQTS, admitted after a sudden cardiac arrest andtotally recovered with implantable cardiac defibrillator (ICD), was focused on

Keywords:

Congenital long QT syndrome, sudden cardiac arrest, implantable cardiacdefibrillator,

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