Esra Sena GENÇ, Abdullah GENÇ, Neşe GÜVENEROĞLU ÜSTÜN

Personality changes in a patient with Wilson’s disease

Wilson Hastalığı (WH), karaciğer ve beyni tutan, sıklıkla adolesan çağda başlayan, nadir görülen bir hastalıktır. WH’nin psikiyatrik belirti ve bulguları da oldukça dikkat çekicidir ve birçok olguda başlangıç belirtisi olarak ortaya çıkar. WH psikiyatrik belirtilerle ortaya çıktığında, tanı gecikmesi yaşanması sıktır. Bu yazıda, tremor ve depresyonla başlayan, sonrasında kalıcı kişilik ve davranış değişikliklerinin geliştiği bir WH olgusu sunulmuştur.

Wilson hastalığına bağlı kişilik değişikliği olgusu

Wilson’s disease (WD) is a rare disorder that primarily affects liver and brain, with the onset frequently in adolescence. Psychiatric symptoms are remarkable and the first manifestation in most cases. WD, when first presented with psychiatric symptoms, delay in the diagnosis can often occurs. This study describes a case of WD starting with tremor and depression and developing permanent personality and behavioral changes later.

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