Meral TORUN BAYRAM, Erhan BAYRAM, Alper SOYLU, Handan ÇAKMAKÇI, Mehmet TÜRKMEN, Semra HIZ KURUL, Salih KAVUKÇU

TÜBEROSKLEROZİS KOMPLEKS AYIRICI TANISINDA RENAL ANJİOMYOLİPOMUN ÖNEMİ

Renal anjiomyolipom, yağ dokusu, kas dokusu ve vasküler yapıları değişik oranlarda barındıran, iyi huylu bir tümördür. Çocukluk çağında seyrek görülür ve renal kitlelerin %3'üdür. Renal anjiomyolipoma genellikle asemptomatiktir ve tesadüfi olarak saptanır. Ancak, Tüberosklerozis kompleks hastalağınının bir parçası da olabilir ve bu hastalarda %50-75 oranında görülür. Bu nedenle, renal anjiomyolipomu bulunan olgularda Tüberosklerozis kompleks ekarte edilmelidir. Obezite ve nonspesifik karın ağrısı nedeniyle yapılan tetkiklerinde tesadüfi olarak renal anjiomyolipom saptanan ve Tüberosklerozis kompleks için yapılan değerlendirmelerinde destekleyici bulgu saptanmayan iki olgu, Tüberosklerozis kompleks kriterlerinin takipte de gelişebilecek olması nedeniyle takip edilmektedir

The Importance Of Renal Angiomyolipoma In The Differential Diagnosis Of The Tuberous Sclerosis

Renal angiomyolipoma is a benign tumour containing adipose tissue, muscular tissue and vascular structures in different ratios. It consists of 3% of the kidney masses and is rarely seen in childhood. Renal angiomyolipoma is usually asymptomatic and detected incidentally. However, it may be a part of tuberous sclerosis complex disease and is seen in 50-75% of these patients. Thus, tuberous sclerosis complex disease should be excluded in cases with renal angiomyolipoma. We present two cases with renal angiomyolipoma detected incidentally upon evaluation for obesity and nonspecific abdominal pain. Although evaluation for tuberous sclerosis complex disease were negative at the moment, they are being followed up with respect to the development of other criteria for tuberous sclerosis complex disease

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