Cahide YILMAZ, Fatmagül BAŞARSLAN, Ahmet Sami GÜVEN, Hüseyin ÇAKSEN, Ahmet Faik ÖNER, Nebi YILMAZ

Lomber ponksiyon sonrası paraparezi ile belirti veren Hemofili A olgusu

Hemofili A da büyük eklem içi kanamalar sık görülmesinin yanısıra, nadiren spinal eklemlerde de oluşabilir. Travmatik ya da spontan hematomların yanısıra kordun baskılanması, epidural tümor ve infeksiyonlar, myeloskleroz, hemolitik anemi ve talasemi gibi kemik iliğinde büyüme yaparak kemik dokuyu bastıran pek çok nedenlerle oluşabilir. Bu çalışmada lomber ponksiyon sonrası gelişen hematomun yaptığı spinal kompresyon sonucu paraparezi gelişen 6 aylık erkek olgunun yapılan incelemesi ile ilk Hemofili A tanısı konulması üzerine sunuldu. Amacımız bu vaka ile perispinal hematomun parapareziye yol açabileceğini ve hemofili A olgularında görülen nörolojik gerilemenin buna bağlı olabileceğini vurgulamaktır.

Anahtar Kelimeler:

Hemofili, paraparezi, çocuk, lomber ponksiyon

A case of Hemophilia A presenting with paraparesis following lumbar puncture

Besides large intra-joint bleedings that are frequently observed in Hemophilia A, bleeding may also rarely occur in spinal joints. Additional to traumatic or spontaneous hematomas, cord suppression may be occured due to various reasons such as epidural tumor and infections, myelosclerosis and bone tissue suppression that occurs to the enlargement in the bone marrow because of hemolytic anemia and thalassemia. In the present study a 6 months old male who developed paraparesis as a result of spinal compression of a hematoma that occurred after lumbar puncture and then diagnosed with Hemophilia A presented on account of the present case, our aim is to emphasize that perispinal hematoma may lead to paraparesis and that paraparesis may develop due to neurological retention that is rarely seen in children with Hemophilia A.

Keywords:

Hemophilia, Paraparesis, Children, Spinal Puncture,

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