İzole ve kompleks kardiyak defektli inferiyor vena kava anomalisi olan iki olgu

İnferiyor vena kava anomalileri nadir görülen konjenital anomalilerdir. Birçok farklı semptomla ortaya çıkabilmelerine rağmen, genellikle asemptomatiklerdir ve eşlik ettiği konjenital kalp anomalilerinin incelenmesi sırasında rastlantısal olarak saptanabilirler. Kardiyak anjiyografi ve açık kalp cerrahisi gibi invaziv işlemlerden önce bu anomalilerin saptanması, zaman kaybı ve beklenmeyen komplikasyonların önlenmesi açısından önemlidir. Ekokardiyografide transabdominal kesitte saptanan, anjiyografi yapılan, biri izole, diğeri atriyo- ventriküler septal defekt ile birlikte olan, her ikisinde de suprarenal inferiyor vena kava yokluğu ve vena azigos devamlığı saptanan iki olgu sunuldu.

Two cases with isolated and complex cardiac defects together with inferior vena cava anomaly

Systemic venous anomalies are rare congenital anomalies. Although they appear in different symptoms, they are usually asymptomatic and they can be detected incidentally during investigation of other congenital heart anomalies. The knowledge of this kind of anomalies before cardiac angiography and open heart surgery is important to prevent time loss and unexpected complications. Echocardiography transabdominal view is used and angiography is performed for confirmation. We report two cases in which absent suprarenal inferior vena cava with vena azygos continuity was present. One is isolated and one is present with cardiac atrioventricular septal defect.

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Dicle Tıp Dergisi-Cover
  • ISSN: 1300-2945
  • Yayın Aralığı: Yılda 4 Sayı
  • Başlangıç: 1963
  • Yayıncı: Cahfer GÜLOĞLU
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