Ahmet KUTLUHAN, Mehdi SALVİZ, Akif Sinan BİLGEN, Hüseyin ÇETİN

Two unusual case of congenital conductive hearing loss related to anomaly of stapes

Konjenital anomaliler izole kemikçik anomalisi halinde veya dış kulakla kombine anomali olarak görülebilir. İzole kemikçik anomalisi klinik pratikte çok ender olarak rastlanır. Bu anomalilerle ilgili literatürün çoğunluğunu vaka takdimleri oluşturmaktadır ve vaka serisi halindeki bildiriler oldukça sınırlıdır. Konjenital ossiküler anomalinin tedavisi kemikçiklerdeki ve oval penceredeki anomalinin varlığına ve biçimine bağlı olarak değişiklik göstermektedir. Bu makalede ileri derecede oval pencere anomalisi ve hareketli tabanla birlikte stapes suprastriktürünün yokluğu ile karakterize iki ender olgunu ve tedavisi literatür taraması ışığında sunulmuştur.

Konjenital stapes anomalisine bağlı iletim tipi işitme kayıplı nadir iki olgunun sunumu

Congenital abnormalities may occur in an isolated form of congenital ossicular or combined with external ear. Isolated ossicular anomalies are rarely seen in clinical practice only, a few reports include series of patients and vast majority of publications are consisted of case reports. Treatment of congenital ossicular anomalies depends on the condition of ossicular and oval window anomalies. In presented article two case reports with severe oval window anomalies and absence of suprastructure of stapes with mobile footplate were published. Management of these cases was discussed with the review of the literature.

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