Primer ovaryan leimyosarkom

Over leimyosarkomu çok kötü prognozlu agresif nadir bir tümördür. Uterin tümörlerin aksine ovaryan düz kas tümörleri, yumurtalık tümörlerinin sadece% 1'ini içeren çok nadir tümörlerdir. Ovaryan leimyosarkom genellikle postmenapozal periyotta görülür. Ancak bu vakada olduğu gibi premenapozal periyottada tanı konabilir. Primer pür ovaryan leimyosarkomlar ovaryan düz kas hücreli tümörlerin malign alt grubunu oluşturur. Bu nedenle kökenleri, etiyolojisi, histolojik özellikleri, klinik davranışları ve optimal tedavileri hala belirsizdir. 59 yaşında bir hasta, karnında kitle ve ağrı şikayeti ile hastanemize başvurdu. Ameliyat öncesi çeklen abdominal ultrasonografi ve bilgisayarlı tomografide tüm abdomeni dolduran kitle tespit edildi.Total histerektomi, bilateral salpingo-ooferektomi, omentektomi, appendektomi, bilateral pelvik ve paraaortik lenf nodu diseksiyonu ve peritoneal yıkama yapıldı. Histopatolojik incelemede primer ovaryan leimyosarkom tespit edildi. Bildiğimiz kadarıyla mevcut vakamızla birlikte literatürde 73 vaka bildirilmiştir.

Primary leimyosarcoma of the ovary

Ovarian leimyosarcoma is a rare aggressive tumor with a very bad prognosis. Contrary to their uterine counterparts, ovarian smooth muscle tumors are extremely rare comprising only 1% of ovarian tumors. Ovarian leimyosarcoma is generally seen in the postmenopausal period. Here we report a 59-year old patient diagnosed as as ovarian primary leimyosarcoma.

Keywords:

Ovarian neoplasm sarcoma, leimyosarcoma,

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