Ayşenur ACAR, ONUR BALABAN, İlker İTAL, TAYFUN AYDIN

POLAND SENDROMLU OLGUDA ANESTEZİ YÖNETİMİ VE ULTRASON EŞLİĞİNDE İNFRAKLAVİKULER BLOK UYGULAMASI

Poland sendromu pektoral kasın yokluğu, farklı göğüs deformiteri ve el anomalileri ile karakterize nadir bir doğumsalanomalidir. Özellikle göğüs duvarı deformiteleri, genel anestezi sırasında solunumsal komplikasyonlara neden olabilir. Budeformiteler rejyonel anestezi-analjezi uygulamalarını da zorlaştırabilir. Bu olgu sunumunda humerus fraktürü nedeniyleoperasyonu planlanan Poland Sendromlu 43 yaşında erkek hastanın perioperatif anestezi yönetimi tartışıldı. Olguya postroperatifanaljezi amaçlı ultrason eşliğinde infraklavikular blok uygulandı.

ANESTHESIA MANAGEMENT OF POLAND SYNDROME ANDINFRACLAVICULAR BLOCK APPLICATION WITH ULTRASONOGRAPHY

Poland Syndrome is a very rare congenital disorder which is usually characterized by underdevelopment or absence of pectoralmuscles, chest and hand anomalies. Especially, chest deformity may lead to respiratory complications during performance of generalanesthesia. Anatomical deformities may also cause difficulty of regional anesthesia procedures. Here, we present the case of a 43year old Poland syndrome patient and discussed his anesthetic management. Ultrasound guided infraclavicular block wasperformed for postoperative analgesia.

PDF

___

1. Stevens DB, Fink BA, Prevel C. Poland's syndrome in one identical twin. J Pediatr Orthop 2000; 20: 392-395.
2. Van Steensel MA. Poland anomaly: not unilateral or bilateral but mosaic. Am J Med Genet A 2004 1; 125A: 211-212.
3. Bavinck JN, Weaver DD. Subclavian artery supply disruption sequence: hypothesis of a vascular etiology for Poland, Klippel-Feil, and Möbius anomalies. Am J Med Genet 1986; 23: 903-918.
4. Bouwes Bavinck JN, Weaver D. Subclavian artery supply disruption sequence: hypothesis of a vascular etiology for Poland, Klippel-Feil, and Mobius anomalies. Am J Med Genet 1986; 23: 903-918.
5. Pereira LH, Sabatovich O, Santana KP, Picanço R, Sterodimas A. Surgical correction of Poland's syndrome in males - a purposely designed implant. J Plast Reconstr Aesthet Surg 2008; 61:393-399.
6. Fokin AA, Robicsek F. Poland's syndrome revisited. Ann Thorac Surg 2002; 74: 2218-2225.
7. Al-Qattan MM. Classification of hand anomalies in Poland's syndrome. Br J Plast Surg 2001; 54: 132-136.
8. Jones KL. Smith's Recognizable Patterns of Human Malformation. 5th ed. Philadelphia: Elsevier Saunders, 1997: 302.
9. Kabukcu HK, Sahin N, Kanevetci BN, Titiz TA, Bayezid O. Anaesthetic management of patient with Poland syndrome and rheumatic mitral valve stenosis: a case report. Ann Card Anaesth 2005; 8: 145-147.