Ahmet Selim ÖZKAN, Sedat AKBAŞ, Mehmet Rıdvan YALIN, Emine ÖZDEMİR

Seckel Sendromlu Olguda C-Mac Videolaringoskop ile Nazotrakeal Entübasyon

Seckel Sendromu; mikrosefali, retrognati ve tipik yüz görünümü nedeniyle zor havayoluna neden olabilen nadir bir otozomal hastalıktır. Seckel Sendrom’lu hastaların anestezi yönetiminde zor damar yolu erişimi başta olmak üzere gelişen zor havayolu gibi durumlarda gerekli önlemlerin alınması önemlidir ve alternatif havayolu araçlarının da havayolunu sağlamada yardımcı olabileceği unutulmamalıdır.

Anahtar Kelimeler:

Seckel Sendromu, videolaringoskop, nazotrakeal entübasyon

Nasotracheal Intubation of a Patient with Seckel Syndrome by C-Mac Videolaryngoscope

Seckel Syndrome is a rare autosomal disease that can cause difficult airway because of microcephaly, retrognathia, and typical facial appearance. It is important to take the necessary precautions in cases such as patients with Seckel Syndrome which especially require difficult venous access and difficult airway in anesthesia management and it should not be forgotten that alternative airway vehicles may also assist the airway management.

Keywords:

Seckel Syndrome, videolaryngoscope, nasotracheal intubation,

PDF

___

Referans1.Seckel HPG. Bird-headed dwarfs:studies indevelopmental anthropology including human proportions. Springfield: Charles C. Thomas; 1960.
Referans2.Parent P, Moulin S, Munck MR, et al. Bird headed dwarfism in Seckel Syndrome Nosologic difficulties. Arch Pediatr 1996;3:55-62.
Referans3.Gurkan Y, Hosten T, Dayioglu H, et al. Anesthesia for Seckel Syndrome. Pediatr Anesth 2006;16:359-60.
Referans4.Sophie S, Ahmed T. Dialysis access surgery with Seckel Syndrome. Paediatr Anesth 2006;16:804-5.
Referans5.Grewal A, Sood D, Bhatia N, Garg R, Shah S, Kaur H. Palatoplasty in a patient with Seckel syndrome: an anesthetic challenge. Braz J Anesthesiol 2014;64(3):216-8. doi: 10.1016/j.bjane.2013.08.005.
Referans6.Demiralp G, Mayhew J. Anesthesia in a child with Seckel syndrome. Paediatr Anaesth 2007:;17(11):1121.
Referans7.Arora S, Ghai B, Rattan V. Anesthetic management of a child with Seckel syndrome for multiple extractions and restoration of teeth. J Anaesthesiol Clin Pharmacol 2012;28(3):398-9. doi: 10.4103/0970-9185.98361.