ERAY ATALAY, HALİL İBRAHİM ERDOĞDU, Bilge Kağan TUR, Mehmet Tamer ÖZDEMİR

Protein kaybettiren enteropati ile presente olan intestinal lenfanjiomatozis

Lenfanjioma lenfatik sistemde proliferasyon ve genişleme ile karakterize bir benign tümördür. Lenfanjiomalar submukozal tümörlerdir, endotel ile kaplı lenfatik alan, lenfatik doku ve düz kas içerirler. Beyin dokusu lenfatik sistem içermediği için beyinde görülmez, bunun dışında bütün organları etkileyebilmektedir. Her organda görülebilmesine karşın yetişkin hastalarda ve intestinal tutulum çok nadirdir. Bu vakada pretibial ödem ve hipoalbuminemisi olan 44 yaşında bayan hasta anlatılmıştır. Batın ultrasonografisinde minimal serbest sıvı görüldü. Tomografide ileumda segmental duvar kalınlaşması bulundu. Hastaya kapsül endoskopi ile intestinal lenfanjiomatozis tanısı konuldu.

Anahtar Kelimeler:

Protein kaybettirici enteropati, lenfanjioma

Intestinal lymphangiomatosis presenting with protein-losing enteropathy

Lymphangioma is a benign tumor characterized by proliferation and dilatation of lymph vessels. Lymphangiomas are submucosal tumors consisting of an endothelial lining with lymphatic spaces, lymphoid tissue, and smooth muscle. They can affect all the organs except the brain, because the brain does not contain a lymphatic system. Although this disease can be seen in any organ, intestinal presentation in an adult is very rare. In this case report, we present a 44-year-old woman with pretibial edema and hypoalbuminemia. Abdominal ultrasonography showed minimal free fluid, and a computed tomography scan showed segmental wall thickening of the ileum. The patient was diagnosed with intestinal lymphangiomatosis by capsule endoscopy.

Keywords:

Protein-losing enteropathy, lymphangioma,

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