HUNTINGTON KORE OLGUSUNDA BAŞARILI ANESTEZİ YÖNETİMİ VE DERLENMEDE SUGAMMADEKS KULLANIMI-OLGU SUNUMU

Huntington koresi (HK) otozomal dominant geçişli, ilerleyici özellikte bir hastalıktır ve bazal ganglionların ilerleyici şekilde etkilenmesi ile ortaya çıkar. Hastalarda regürjitasyon ve pulmoner aspirasyon riskinde artma, uzamış tiyopental ve süksinilkolin cevabı, solunum güçlüğü, rijit spazma kadar ilerleyebilen postoperatif titreme gibi komplikasyonlarla karşılaşılabilir. Prevalansı 100000 de 4-10 olan bu hastalıkla ilişkili olarak literatürde bildirilen anestezi yöntemleri sınırlı olguda denenmiştir. Olgu sunumumuzda HK hastalığı olan 50 yaşında erkek hastanın anestezi yönetimini sunmayı amaçladık. Antikolinesteraz kullanımından kaçınmak amacıyla 100 mg sugammadeks verilen hasta başarılı bir şekilde ekstübe edildi ve derlenmesi sağlandı.

Anahtar Kelimeler:

Huntington hastalığı, anestezi yönetimi, sugammadeks

SUCCESSFUL ANESTHETIC MANAGEMENT AND RECOVERY WITH SUGAMMADEX IN A PATIENT WITH HUNTINGTON’S CHOREA-A CASE REPORT

ABSTRACTHuntington’s chorea (HC) is an autosomal dominant hereditary disease with progressive characteristics affecting the basal ganglia. Patients may encounter complications like increased risk of regurgitation and pulmonary aspiration, prolonged thiopental and succinylcholine response, respiratory difficulties and postoperative shivering advancing to rigid spasms. With a prevalence of 4-10/100.000, there are limited case reports about anesthetic methods for this disease in the literature. In our case report, we aimed to present the anesthetic management of a 50-year old male patient with HC disease. Avoiding the use of anticholinesterase, 100 mg sugammadex was administered, the patient was successfully extubated and recovery was ensured.

Keywords:

Huntington disease, anesthetic management, sugammadex,

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