Gökhan PEKER, Sunkar KAYA BAYRAK, Alkan BAYRAK, Dila METE PEKER

Falanks Enkondromunun Osteopoıkılozlu Kemikten Alınan Otogreft ile Tedavisi: Olgu Sunumu

Osteopoikiloz, çocukluk çağında gelişmeye başlayan ve ileri yaşlarda devam eden, enkondral kemik matürasyonunda anormallikle karakterize, nadir görülen bir kemik displazisidir. Sıklıkla asemptomatik olmakla beraber genellikle rastlantısal olarak saptanır. Otozomal dominant geçişli olan patoloji, sporadik olarak da görülebilmektedir. Enkondrom ise klasik olarak hiyalin kıkırdak kökenli benign, ayak ve el kemikleri gibi küçük kemiklerde yerleşmiş olan uzunlamasına ve oval kemik lezyonlarıdır. Bu çalışmamızda, osteopoikiloz tanılı ve falanksında enkondrom oluşan olgumuzu sunmayı ve tedavisini tartışmayı amaçladık.

Anahtar Kelimeler:

osteopoikiloz, enkondrom, falanks

Treatment Of Phalanx Enchondroma By Autograft Harvested From The Bone With Osteopoikilosis: A Case Report

Osteopoikilosis is a rare bone dysplasia characterized by abnormally enchondral bone maturation, which generally stars to be formed in the childhood and continues in the adulthood. It is generally asemptomatic and it is determined incidentally. As it is generally inherited otosomal dominantly, sporadic cases can also be seen. Enchondroma is a benign lesion formed from hyaline cartilage mostly in small bones like foot and hand with longitudinal and elliptic shape. In this study, we would like to discuss the patient with phalangeal enchondroma and osteopoikilosis.

Keywords:

osteopoikilosis, enchondroma, phalanx,

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