Wilson Hastalığının Nadir Bir Komplikasyonu: Hepatoselüler Karsinom

Bakır metabolizma bozukluğu olan Wilson hastalığı, klinik spektrumu oldukça geniştir. Birikim yaptığı organa spesifik bulgu vermektedir. Bu hastalar gastroenteroloji polikliniğinde asemptomatik transaminaz yüksekliği ile başvurabileceği gibi, ileri komplikasyonlardan olan siroz ve hepatoselüler karsinom şeklinde de prezente olabilmektedir. Olgu sunumunda siroz nedeniyle takipli olan Wilson hastasının rutin takiplerinde AFP (alfa-feto protein) yüksekliği olması nedeniyle ileri araştırmalar sonucunda HCC (hepatoselüler karsinom) tanısı alan hastayı sunmaktayız.

Anahtar Kelimeler:

Wilson, Hepatoselüler Karsinom, Siroz, Hepatocelüler Carcinoma, Cirrhosis

A Rare Complication of Wilson's Disease: Hepatocellular Carcinoma

Wilson's disease, which is a disorder of copper metabolism, its clinical spectrum is quite wide. It gives specific findings to the organ it accumulates. These patients may present with asymptomatic transaminase elevation in the gastroenterology outpatient clinic, as well as cirrhosis and hepatocellular carcinoma, which are advanced complications. In the case report, we present a patient who was diagnosed with HCC (hepatocellular carcinoma) as a result of advanced research due to the high AFP (alpha-feto protein) during routine follow-up of a Wilson patient who was being followed up due to cirrhosis.

Keywords:

Hepatocelüler Carcinoma, Cirrhosis,

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