Ebru Alici DAVUTOGLU, Ayşegül ÖZEL, HAKAN ERENEL, Rıza MADAZLI

Ailevi Akdeniz Ateşi Olan 40 Gebenin Perinatal Sonuçları

Amaç : Ailevi Akdeniz Ateşi (AAA) tanısı olan, gebe olguların maternal ve fetal sonuçlarının değerlendirilmesi amaçlanmıştır. Gereç ve Yöntem : Çalışmamız 2013-2017 yılları arasında üniversitemizin perinataloji kliniğinde gebelikleri takip edilmiş 40 AAA olgusunun dosya verilerinin retrospektif olarak incelenmesiyle yapıldı. Hastaların klinik özellikleri , obstetrik ve perinatal sonuçları değerlendirildi. Bulgular: Ortalama hasta yaşı 30.75 ±6.15, nulliparite oranı %42,5 bulundu. Ortalama hastalık süresi 8,36 ± 5.44 yıl olarak bulundu. Gebelik sırasında 7 hasta atak geçirdi. Hastaların % 90 ’ ı medikal tedavi almaktaydı. Ortalama doğum haftası 37,3±4.5, ortalama doğum kilosu 3115±547 gr bulundu. Preterm doğum, fetal büyüme kısıtlılığı ,preeklampsi görülme oranları sırasıyla; %10 , %5 , %10, olarak bulundu. Fetal ve neonatal kayıp, ile konjenital anomalili doğum gözlenmedi. Sonuç : AAA tanılı gebelik olgularının yönetiminde multidisipliner yaklaşım ile takip ve tedavinin sağlanması olumlu maternal ve fetal sonuçlar ile ilişkilidir.

Anahtar Kelimeler:

Ailevi Akdeniz Ateşi ; perinatal sonuçlar

Perinatal Outcomes of 40 Pregnancies with Familial Mediterranean Fever

Objective : To evaluate maternal and fetal outcomes of pregnancies diagnosed with Familial Mediterranean Fever (FMF) Methods : Retrospective analysis of 40 pregnancies diagnosed with FMF who received antenatal care at our perinatology unit between 2012 -2017 included in this clinical study. Clinical characteristics of patients, perinatal and maternal outcomes were evaluated. Results : The mean patient age was 30.75 ±6.15 and the nulliparity rate was 42,5 %. The mean duration of illness was found to be 8,36 ± 5.44 years. 7 patients had an attack during pregnancy. 90 % of the patients received medical treatment. Mean gestational age at delivery was 37,3±4.5 , mean birth weight was 3115±547 g. Preterm delivery, fetal growth restriction and preeclampsia rates were 10, 5, 10 % respectively. Fetal and neonatal loss, congenital anomalous birth was not observed. Conclusion: Multidisciplinary approach to the care of pregnancy diagnosed with FMF is associated with good maternal and fetal outcomes.

Keywords:

: Familial Mediterranean Fever ; perinatal outcome,

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