Castleman Hastalığı: Laparoskopik Yaklaşımla Tedavi Edilen Pararenal Alanda Nadir Bir Retroperitoneal Kitle
Unicentric Castleman Hastalığı (UCD), etiyolojisi bilinmeyen nadir bir hastalıktır. UCD, lokalize lenfoid doku proliferasyonu ve interfoliküler hipervaskülarite ile karakterizedir. Pararenal alanda, diğer tümörleri taklit edebilen nadir görülen bir kitledir. Bu vakada kliniğimizde laparoskopik yaklaşımla tedavi edilen retroperitoneal UCD'yi sunuyoruz.
Castleman’s Disease: A Rare Retroperitoneal Mass In The Pararenal Space Treated With Laparoscopic Approach
Unicentric Castleman’s Disease (UCD) is a rare disorder with unknown etiology. UCD is characterized by a localized lymphoid tissue proliferation and interfollicular hypervascularity. It is a rarely seen mass in the pararenal space, which can mimic other tumors. In this case, we present a retroperitoneal UCD which is treated with laparoscopic approach in our clinic
___
- Referans 1. Mantas D, Damaskos C, Dailiani P, Samarkos M,Korkolopoulou P. Castleman’s disease of the spleen. ActaChirBelg2016;117:203–8.
- Referans 2. Casper C. The aetiology and management of Castleman diseaseat 50 years: translating pathophysiology to patientcare. Br J Haematol2005;129:3–17.
- Referans 3. Yi Xie, Yi Zhao, Zhi-Gang Ji, Han-Zhong Li, Guang-Hua Liu, Quan-Zhong MaoCastleman's Disease: A Rare Mass in the Pararenal Retroperitoneum that Mimics Other Tumors. Chinise medical journal 2017 ;130-17
- Referans 4. Bracale U, Pacelli F, Milone M, Bracale UM, Sodo M, Merola G, et al. Laparoscopic treatment of abdominal unicentric Castleman’s disease: a case report and literature review. BMC Surg2017;17:38.
- Referans 5. El-Osta HE, Kurzrock R. Castleman’s disease: from basicmechanisms to molecular therapeutics. Oncologist 2011;16:497–511.