A.c. ERDAL, M. KIR, E. SİLİSTİRELİ, Ö. KARABAY, O. SERBEST, Ü. AÇIKEL

Çocukluk çağı semptomatik aberran sağ subkavyan arter: Bir olgu sunumu

Amaç: Aberran sağ subclavyan arter, sol aortik arkus varlığında sık görülen doğumsal aort anomalilerindendir. Geniş otopsi dizilerinde olguların % 0.7’ sinde bulunduğu belirlenmiştir. Ancak aberran sağ subklavyan arter, vasküler ring oluşumları dışında ender olarak çocukluk çağında bulgu verir. Olgu sunumu: Ondört aylık erkek çocuk hırıltı, solunum sıkıntısı, beslenme güçlüğü ve gelişme geriliği yakınmaları ile hastanemize başvurdu. Göğüs posterio-anterior grafisi, magnetic rezonans görüntüleme, anjiografi yapıldı ve semptomların aberran sağ subklavyan arterden kaynaklandığı belirlendi. Sonuç: Sol posterolateral torakotomi yapılan olguda, aberran sağ subklavyan arter, arkus aortadan reseke edilerek, çıkan aortaya anastomoz edildi. Operasyon sonrası dönem sorunsuz geçirildi ve tüm operasyon öncesi was uneventful and all preoperative symptoms semptomlar postoperatif altıncı ayda kayboldu. disappeared within six months postoperatively

Anahtar Kelimeler:

Sol arkus aorta, aberran sağ subklavyan arter, arkus aorta anomalileri

Symptomatic abberant right subclavian artery at the childhood period: A case report

Purpose: The abberant right subclavian artery, in the existance of left archus aorta, is a common congenital aortic anomaly and has been reported to occur in 0.7% of the population in large autopsy series. However, if the aberrant right subclavian artery does not take place in a vascular ring formation, it is rarely symptomatic at the childhood period. Case report: A fourteen-months-old boy was attempted to the hospital with the complaints of wheezing; difficulty in breathing and failure of thrive. Chest X-ray, Magnetic resonance imaging and angiographies were performed and it was determined that symptoms were resulted from aberrant right subclavian artery. Conclusion: The case underwent a left posteriolateral thoracotomy; the aberrant right subclavian artery was resected from the archus aorta and anastomosis was done to the ascendant aorta. The post-operative period

Keywords:

Left aortic arch, aberrant right subclavian artery, anomaly of the archus aorta,

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