Sinem AKBAY, Şule CAN, Tunç ÖZDEMİR, Bumin Nuri DÜNDAR, Kıvanç ÇELİKKALAN

Tek Paratiroid Adenomuna Bağlı Hiperparatiroidizm: Olgu Sunumu

Hiperparatiroidizm çocukluk çağında çok nadir görülen bir hastalıktır. Genellikle bulantı, kusma, kabızlık, irritabilite, letarji, başağrısı, poliüri ve polidipsi gibi özgül olmayan semptomlarla başvurulmakta ve bu nedenle tanı konulması gecikebilmektedir. Tanı klinik inceleme ve laboratuvar bulguları ile konulur. Görüntüleme yöntemleri ile paratiroid hiperplazisi ve adenomu ayrımı yapılmaktadır. Hipokalsiürik hiperkalsemi ile karışabileceğinden idrar kalsiyum düzeylerine bakılması ayırıcı tanıda önemlidir. Paratiroid adenomunun kesin tedavisi adenomun çıkartılmasıdır. Ayrıca, kemik tutulumu ve uç organ hasarı yönünden dikkatli olunmalıdır. Burada, acil servise bulantı ve kusma yakınması ile başvuran, hiperparatiroidiye bağlı hiperkalsemi tespit edilen ve paratiroid sintigrafisi ile tiroid lojunun sağ alt kesiminde tek paratiroid adenomu saptanan 12 yaşındaki erkek olgu sunulmuştur.

Anahtar Kelimeler:

Çocukluk çağı, Hiperkalsemi, Hiperparatiroidi, Paratiroid adenomu

Hyperparathyroidism due to a Parathyroid Adenoma: Case Report

Hyperparathyroidism is very rare disorder in childhood. Patients usually present with non-specifi c symptoms such as nausea, vomiting, constipation, irritability, lethargy, headache, polyuria and polydipsia, and the diagnosis can therefore be delayed. Diagnosis is made by clinical examination and laboratory fi ndings. Parathyroid hyperplasia and adenomas can be differentiated with imaging methods. Hypocalciuric hypercalcemia may have similar fi ndings and investigating urine calcium levels is important for the differential diagnosis. Defi nitive treatment of a parathyroid adenoma is removal of the adenoma. End organ damage such as bone changes and nephrocalcinosis should be kept in mind. We discuss a 12-year-old boy who had hypercalcemia due to hyperparathyroidism. He presented at our emergency department because of nausea and vomiting and was diagnosed with a solitary parathyroid adenoma located on the lower right side of the thyroid gland by using parathyroid scintigraphy

Keywords:

Childhood, Hypercalcemia, Hyperparathyroidism, Parathyroid adenoma,

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