İpek AKIL, Muzaffer POLAT, Serdar TARHAN, Yılmaz Gülgün OVALI, Petek BAYINDIR

Co-occurrence of internal carotid artery agenesis with multicystic dysplastic kidney

Özet: İnternal karotid arterin (İKA) yokluğu nadir bir durumdur. Bu anomali izole görülebileceği gibi diğer organ ve sistem anomalileri ile birliktelik gösterebilir (1). Multikistik displastik böbrek (MKDB) renal korteksin değişik boyutta birçok kist ile kaplanması ile karakterize konjenital bir hastalıktır. Ürolojik ve non ürolojik anomaliler MKDB‘e eşlik edebilir (2). İKA yokluğuna multikistik displastik böbrek anomalisinin eşlik ettiği olgumuz sunulmaktadır. Bilgimize göre olgumuz literatürde İKA yokluğu ve MKDB birlikteliğinin ilk sunulmuş formudur.

İnternal karotid arter agenezisi ve multikistik displastik böbrek anomalisinin birlikteliği

Abstract: Congenital absence of Internal Carotid Artery (ICA) is a rare disorder. This anomaly may be an isolated entity or may be associated with other organ, or system anomalies (1). Multicystic Dysplastic Kidney (MCDK) is a congenital mal-development in which the renal cortex is replaced by numerous cysts of multiple sizes. Urologic and non-urologic anomalies may accompany MCDK (2). In this paper, we detail a case of congenital agenesis of ICA and the existence of MCDK. To our knowledge, this is the first of such a case to be reported regarding the co-occurrence of ICA agenesis and MCDK.

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