Alper GÜZELTAŞ, Murat SAYGI, Eyüp ASLAN, Erkut ÖZTÜRK, İbrahim Cansaran TANIDIR

Transcatheter management of obstructed pulmonary venous return and pulmonary atresia in a newborn with heterotaxy syndrome

Heterotaksi sendromu, birçok intrakardiyak gelişim anomalisinin eşlik ettiği kompleks kardiyak patolojilerdir. Bu hastalardaki başlıca sorunlardan biri, total anormal pulmoner venöz bağlantıdır. Yenidoğanlarda patent duktus arteriyozus stenti birçok merkezde uygulanabilmesine rağmen, tıkalı total anormal pulmoner venöz bağlantıda vertikal ven stenti iyi tanımlanmış bir işlem değildir. Bu yazıda tıkalı suprakardiyak total anormal pulmoner venöz bağlantı ve pulmoner atrezisi olan, transkateter palyasyon ile başarılı bir şekilde tedavi edilen bir yenidoğan olgu sunuldu.

Heterotaksi sendromlu bir yenidoğanda tıkalı pulmoner venöz dönüş ve pulmoner atrezinin transkateter tedavisi

Heterotaxy syndrome refers to complex cardiac pathologies accompanied by several intracardiac development abnormalities. One of the main problems in these patients is total abnormal pulmonary venous connection. Although stenting the patent ductus arteriosus in newborns can be performed in several centers, stenting of the vertical vein in obstructed total abnormal pulmonary venous connection is not a well-established procedure. Herein, we report a newborn case with obstructive supracardiac total abnormal pulmonary venous connection and pulmonary atresia who was successfully treated with transcatheter palliation.

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