Yenidoğan döneminde proksimal intestinal atrezi nedeniyle opere edilmiş ve laparotomisinde annüler pankreas, duedonal atrezi ve malrotasyon tanıları alan Down sendromlu bir olgu 13 aylıkken brid ileus nedeniyle tekrar başvurdu. Yapılan operasyonda nekroz nedeniyle rezeke edilen ileum segmentinin histopatolojik muayenesi hyalen vasküler tip Castleman hastalığı olarak rapor edildi. Anahtar kelimeler: Süt Çocuğu, Annüler Pankreas, Castleman Hastalığı, Down Sendromu

A patient with Down syndrome who had an operation for proximal intestinal atresia in the newborn period and had the diagnoses of annular pancreas, duodenal atresia, and malrotation was admitted a second time when he was 13 months old with intestinal obstruction due to adhesions. Histopathology of the resected necrotic ileal segment in the operation was reported as Castleman's disease of hyaline vascular type. Key words: Infant, Annular Pancreas, Castleman's Disease, Down Syndrome