Rıza DOĞAN, Sevgen ÖNDER, Murat KARA, Alkın YAZICIOĞLU

Giant atypical lipomatous tumor of the mediastinum

İyi diferansiye liposarkom olarak da adlandırılan atipik lipomatöz tümörler adipositik tümörlerin ara veya lokal agresif formudur. Bu tümörler mediastende nadiren yerleşir ve eksizyon sonrası potansiyel nüks riski taşır. Bu olgu sunumunda mediastende lokalize olan ve cerrahi olarak eksize edilen dev atipik lipomatöz tümörlü bir hasta sunuyoruz. Hasta nüks gelişmeden postoperatif 17. ayda asemptomatik olarak izlenmektedir. Cerrahi, mediastinal liposarkomların tedavisinde en iyi seçenektir.

Mediastenin dev atipik lipomatöz tümörü

Atypical lipomatous tumors, so-called well differentiated liposarcomas are the intermediate or locally aggressive form of adipocytic tumors. Mediastinum is an uncommon localization for these tumors and they have a potential risk of recurrence following excision. We herein report a case with a giant atypical lipomatous tumor located at the mediastinum that was surgically excised. The patient is free of recurrence and asymptomatic at postoperative 17 months. Surgery remains as the treatment of choice for mediastinal liposarcomas.

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