Lenf nodu metastazlı baş ve boynun çoklu primer malign paragangliyoması
Baş ve boyun paragangliomaları genellikle benign tümörlerdir. Malign form son derece seyrek olup malignite kriterleri açık değildir. Malign formların klinik, biyokimyasal ve histolojik özellikleri onları benign formdan ayırt etmek için yeterli değildir ve malignite ancak uzak metastaz olduğunda saptanabilir. Bu yazıda sağ tarafta glomus jugulare, sol tarafta glomus vagale ve glomus karotikum tümörleri olup sağ tarafta boyun lenf nodu metastazı gösteren bir hasta sunuldu
Anahtar Kelimeler:
Glomus karotikum, glomus jugulare, glomus vagale, malign paraganglioma
Multiple primary malignant paraganglioma of the head and neck with lymph node metastasis
Paragangliomas of the head and neck are usually benign tumors. Malignant form is quite rare and criteria for malignancy are not clear. Clinical, biochemical and histological features of malignant forms are not sufficient to reliably distinguish them from benign tumors and malignancy is established only in the presence of distant metastasis. Herein, we report a patient with glomus jugulare on the right, glomus vagale and glomus caroticum tumors on the left side with cervical lymph node metastasis on the right side.
Keywords:
Glomus caroticum, glomus jugulare, glomus vagale, malignant paraganglioma,
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- ISSN: 2602-4837
- Yayın Aralığı: Yılda 4 Sayı
- Başlangıç: 1991
- Yayıncı: İstanbul Üniversitesi