Türker YÜCESOY, Ahmet YAĞCI, Elif Dilara ŞEKER

Williams Sendromlu hastanın ortodontik tedavisinin sonuçları ve tedavideki zorluklar

Williams Syndrome (WS) nadir görülen ve progresif bir şekilde ilerleyen multi-sistem bir sendrom olup özel sistemik hastalıklarla beraber, iskeletsel ve dental anomalilere ek olarak dil itme durumunun izlenebildiği bir hastalık tipidir. Bu vaka raporunda kliniğimize malokluzyon ve dil itme şikayetiyle başvuran WS sendromlu hastanın tedavisi sırasında karşılaşılan zorluklar ve tedavi planlaması anlatılmaktadır. Hasta standart edgewise braketler(Mini Master Series from American Orthodontics (Central Islip, N.Y., USA),0.018 inch braket slot) ile yaklaşık 2 yıl 8 ay tedavi edilmiştir. Bu vaka raporunda, WS tanısı ile takip edilen hastanın ortodontik tedavisi süresince karşılaşılan zorluklar ve bunlara rağmen elde edilen başarılı sonuçların paylaşılması hedeflenmiştir. Hastanın ortodontik tedavisi kötü oral hijyenine rağmen sık randevu aralıkları sayesinde çürük kaviteleri oluşmadan tamamlanmıştır. Ayrıca hastanın sağlıklı premolar dişlerinin ağızda tutularak prognozu belirsiz molar dişlerinin çekimi sosyal olarak hastaya avantaj sağlamıştır.

Difficulties and treatment outcomes of orthodontic therapy of a patient with Williams Syndrome

Williams Syndrome (WS) is a rare congenital and progressive multisystem disorder which is described with specific systemic disorders, skeletal and dental abnormalities and tongue thrusting. A 13-year-old patient applied to our clinic with complaining dental caries, malocclusion and tongue thrusting. The patient was treated with a full fixed standard edgewise appliance named as Mini Master Series from American Orthodontics (Central Islip, N.Y., USA), 0.018 inch bracket slots) for 2 years and 8 months. Despite poor oral hygiene, frequent appointments helped to complete the orthodontic treatment of the patient without caries formation. Also extraction of first molars with uncertain prognosis provided social benefits when it was compared to healthy premolar extractions. This case report presents the successful results of the orthodontic therapy and difficulties of an orthodontic treatment of a patient who was diagnosed with WS.

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