Levent YAZMALAR, Mustafa Akif SARIYILDIZ, İbrahim BATMAZ, Hüsamettin ÇAVAŞ

İzole Hemihipertrofi (Hemihiperplazi): Bir olgu sunumu ve literatür derlemesi

Hemihipertrofi (hemihiperplazi) kranium, yüz, gövde, ekstremite ve parmakların asimetrik büyümesi ile karakterizedir. İzole olabileceği gibi bazı sendromlarda görülebilmektedir. Hem sendromik hem de izole hemihipertrofide Willms tümörü, hepatoblastom ve adrenal hücre karsinomu gibi embroyonel ve abdominal tümörlerin görülme sıklığı artmıştır. Bizde bu açıdan izole hemihipertrofili olguyu literatür eşliğinde sunuyoruz.

Anahtar Kelimeler:

Hemihipertrofi, Hemihiperplazi, Beckwith-Wiedeman sendromu

Isolated Hemihypertrophy (Hemihyperplasia): A case report and review of the literature

Hemihypertrophy (Hemihyperplasia) is characterized by asymmetric overgrowth of cranium, face, trunk, limbs and digits. It may be an isolated form or it may occur in several syndromes. In both syndromic and isolated hemihypertrophy there are an increased risk of embryonal tumors, most commonly Wilms tumor, although other abdominal tumors such as hepatoblastoma and adrenal cell carcinoma also ocur. Consequently, along with the literature, we present a case of patient with Isolated Hemihypertrophy.

Keywords:

Hemihypertrophy, Hemihyperplasia, Beckwith-Wiedemann syndrome,

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