Ebstein anomalisi olan ve iki kez kardiyak arrest geçiren 11 yaşındaki hastanın başarılı cerrahisi

Ebstein anomalisi, yüksek morbidite ve mortalite oranlarına sahip, nadir görülen bir doğuştan kalp hastalığıdır. Triküspit kapağın işlev bozukluğu ve kısmen atriyalize olmuş sağ ventrikül, hastalığın temel özellikleridir. Hastalar uzun süreli semptomsuz sağkalıma sahip olabilirken, semptomların geniş bir yelpazesi nedeniyle rahim içi ölümle de karşılaşılabilir. Triküspit kapağın yetersizliği ve sağ kalp yetmezliği en başta gelen semptomlardır. Semptomatik hastalarda ameliyat gecikmeden yapılmalıdır. Carpentier’in Ebstein anomalisinin cerrahi tedavisine yaklaşımı, uygulanabilecek yöntemlerden biridir. Bu çalışmada, ameliyattan önce iki kez kardiyak arrest geçiren Ebstein anomalili 11 yaşındaki bir çocuğun Carpentier tekniği ile başarılı cerrahi tedavisi bildirildi.

Anahtar Kelimeler:

Carpentier Tekniği, Ebstein Anomalisi, Cerrahi

Successful surgery of Ebstein’s anomaly of 11-year-old patient after having had two cardiac arrests

Ebstein’s anomaly is a rarely seen congenital heart disease with high morbidity and mortality rates. Impaired function of tricuspid valve and partially atrialized right ventricle are the main characteristics of the disease. Patients may have symptom-free survival for long terms whereas intra uterine death may also be encountered due to wide range of the symptoms. Regurgitation of the tricuspid valve and right-sided heart failure are the foremost symptoms. Surgery must be performed in symptomatic patients without delay. Carpentier’s approach to the surgical treatment of Ebstein’s anomaly is one of the methods that can be applicable. In this study it is reported that successful surgical treatment of 11-year-old child with Ebstein’s anomaly who had two cardiac arrests before operation, by using Carpentier’s technique.

Keywords:

Carpentier's techniuqe, Ebstein's anomaly, Surgery,

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