Barış TEN, Celal BAĞDATOĞLU, Hasan Hüsnü YÜKSEK, Gülhan TEMEL, Yüksel BALCI

Psödotümör serebri ve Chiari malformasyonu Tip 1 birlikteliği

Amaç: Amacımız Psödotümör serebri ve Chiari malformasyonu Tip 1 birlikteliğinin tanısı için farklı radyolojik belirteçler bulabilmektir. Yöntem: 2007-2020 tarihleri arasında radyoloji anabilim dalına Chiari malformasyonu Tip 1 klinik ön tanısıyla yönlendirilip magnetik rezonans görüntüleme ile radyolojik olarak tanısı doğrulanan hastalar geriye dönük olarak değerlendirildi. Hem servikal hem serebral tetkikleri bulunan 49 Chiari malformasyonu Tip 1 hastası ve aynı yaş ve cinsiyetten olan Chiari malformasyonu Tip 1 tanısı olmayan 49 kontrol grubu çalışmaya dahil edildi. Chiari malformasyonu Tip 1 tanılı hastaların Serebral MRG görüntülerinden radyolojik olarak Psödotümör serebri varlığı, Servikal spinal MRG görüntülerinden şiringomyeli varlığı, McRae çizgisine göre serebeller tonsillerin ve obexin mesafesi milimetre cinsinden değerlendirildi. Bulgular: Chiari malformasyonu Tip 1 klinik ve radyolojik tanılı olgularda radyolojik olarak Psödotümör serebri tanısı konulan hastaların konulmayanlara göre serebeller tonsilleri ve Obexi daha aşağı yerleşimlidir ve siringomyeli eşlik etme oranı daha fazla gözükmektedir. Ancak her iki grup arasında istatistiki olarak anlamlı bir farklılık izlenmemektedir. Sonuç: Psödotümör serebri ve Chiari malformasyonu Tip 1 birlikteliği tahmin edildiğinden daha sık görülmektedir. Psödotümör serebri ve Chiari malformasyonu Tip 1 birlikteliğinde tedavi protokülünün farklı olması bu birlikteliğin tanısını koyabilmenin önemini arttırmaktadır. Psödotümör serebri ve Chiari malformasyonu Tip 1 birlikteliğinin tanısında farklı radyolojik belirteçler bulabilmek için daha fazla sayıda radyolojik görüntüleme çalışmalarına ihtiyaç vardır.

Anahtar Kelimeler:

psödotümör serebri, chiari malformasyonu tip 1, birliktelik, radyolojik belirteçler

Coexistence of pseudotumor cerebri and Chiari malformation Type 1

Aim: Our aim was to find different radiological markers for the diagnosis of coexistence of pseudotumor cerebri and Chiari malformation Type 1. Method: Patients who were referred to the Department of Radiology with a clinical preliminary diagnosis of Chiari malformation Type 1 between 2007 and 2020 and whose diagnosis was confirmed radiologically by magnetic resonance imaging were evaluated retrospectively. 49 Chiari malformation Type 1 patients with both cervical and cerebral examinations and 49 control groups of the same age and sex without Chiari malformation Type 1 diagnosis were included in the study. Presence of pseudotumor cerebri radiologically from Cerebral MRI images of patients with Chiari malformation Type 1 diagnosis, presence of syringomyelia from cervical spinal MRI images, and distance of cerebellar tonsils and obex according to McRae line were evaluated in millimeters. Results: In cases with Chiari malformation Type 1 clinical and radiological diagnosis, patients with radiological diagnosis of pseudotumor cerebri had lower cerebellar tonsils and Obex than those who were not, and the rate of accompanying syringomyelia seemed to be higher. However, there was no statistically significant difference between the two groups. Conclusion: Coexistence of pseudotumor cerebri and Chiari malformation Type 1 was more common than expected. The treatment protocol is different in the coexistence of pseudotumor cerebri and Chiari malformation Type 1, therefore this increases the importance of diagnosing the coexistence. Further radiological imaging studies are needed to find different radiological markers in the diagnosis of pseudotumor cerebri and Chiari malformation Type 1 coexistence.

Keywords:

pseudotumor cerebri, chiari malformation type 1, coexistence, radiological markers,

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