Serkan Burç DEŞER, Mustafa Kemal DEMİRAĞ

Mitral Kapak Replasmanı Sonrası Kısmi Pulmoner Venöz Dönüş Anomalisinin Tamiri: Olgu Sunumu Kısmi Pulmoner Venöz Dönüş Anomalisi

Parsiyel pulmoner venöz dönüş anomalisi (PAPVC) nadir görülen bir konjenital hastalıktır. Tüm konjenital kalp kusurları içinde insidans %0,5’dir. Genellikle bu tür doğumsal kalp kusurları sinüs venosus tipi atriyal septal defekt veya patent foramen ovale ile birlikte görülmektedir. Hastalar hayatlarının sonraki dönemlerine kadar asemptomatik olabilmekte (genellikle hemodinamik olarak anlamlı olmayan ve genellikle iyi tolere edilen) ve tesadüfen akciğer filmi, santral venöz kateterin yanlış yerleştirilmesi sonrasında veya otopsi sırasında tanı konulabilmektedir. Açık kalp ameliyatları öncesinde eşlik eden konjenital kalp defektlerinin tanısı çok önemlidir. Biz 1 yıl önce mitral kapak replasmanı ameliyatı öyküsü olan PAPVC tanısı alan 56 yaşındaki kadın hastanın cerrahi tedavisini sunduk.

Repair of a Partial Anomalous Pulmonary Venous Connection After Mitral Valve Replacement: A Case Report

Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital disorder with an incidence 0.5% of all congenital cardiac defects. Usually seen with congenital cardiac defects such as sinus venosus type interatrial septal defects or patent foramen ovale. Patients are asymptomatic until later in life (usually not hemodynamically significant and it is usually well tolerated by patients) and incidentally diagnosed with routine chest film, central catheter misplacement or post mortem examinations. In open hearts surgeries appropriate preoperative diagnosis is crucial for the accompanying congenital heart defects. We report a case of a surgical treatment of PAPVC in a 56 year old woman who had a history of mitral valve replacement surgery 1 year ago.

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