Özgür EKİNCİ, Özlem OKUR, FİKRET AKSOY, GÖKHAN DEMİRAL, Taner EVCİMİK, Haydar YALMAN, Rafet YİĞİTBAŞI

Diagnosis, treatment, radiologic and pathologic findings of splenic angiosarcoma; a case report

Primer splenik anjiosarkomalar dalağın hematopoetik sistemle ilişkili olmayan en sık malign tümörleri(1) olmasına karşın oldukça nadir görülmekte ve prognozu son derece kötüdür(2). Bu tümörlerin seyri oldukça agresif ve ölümcül olup yaygın metastazlar veya dalak rüptürü ile karşımıza çıkarlar(1). Kesin tanı ve tedavi cerrahi ile olur ve rüptür öncesi uygulanan splenektomi yaşam süresini anlamlı şekilde uzatır(5). Primer splenik anjiosarkomalı bir hastanın tanı, radyolojik patolojik bulgular ve tedavisini sunuyoruz.

plenik anjiosarkomanın tanısı, tedavisi, radyolojik ve patolojik bulguları;olgu sunumu

Although primary splenic angiosarcomas are the most common malignant nonhematopoietic tumors of spleen(1) ,they are extremely rare tumors with very poor prognosis(2). These tumors are highly aggressive and lethal,present with widespread metastasis or splenic rupture(1). Definitive diagnosis and treatment is surgical and survival is significantly improved when splenectomy is performed prior to rupture(5). Diagnosis, radiologic and pathologic findings and treatment of a patient with primary splenic angiosarcoma is presented.

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