A giant leiomyoma originating from the rudimentary uterine buds in rokitansky-kuster-hauser syndrome

The development of leiomyoma from the rudimentary buds in Rokitansky -Kuster- Hauser syndrome is extremely rare. Reviewing the literature, we detected only five cases that had been previously reported. We present a case of Rokitansky -Kuster- Hauser syndrome whom we diagnosed and treated a giant leiomyoma with a diameter of 25 cm.