This report presents the congenital malformations found in a prospectively collected series of 10 infants with neural tube defects. Nine of these were stillborns and one was a neonate who died within 24 hours after birth. All of the infants were singletons. Five of them had craniorachischisis totalis, 2 had anencephaly, 2 had encephalocele, and one had very severe form of cerebro-facial dysplasia.