End-stage hypertrophic cardiomyopathy with impressive biventricular hypertrophy: Evaluation with novel echocardiographic modalities
Hipertrofik kardiyomiyopati en sık rastlanan genetik kökenli kalp hastalığıdır. Gençlerde gözlenen ani kardiyak ölümün en sık sebebi olan bu hastalıkta tipik olarak sol, bazen de sağ ventrikülün idiyopatik hipertrofisi gözlenmektedir. Bu çalışmada, belirgin biventriküler hipertrofi bulguları gösteren son dönem hipertrofik kardiyomiyopatili bir olgu yeni ekokardiyografik modaliteler ile incelenmiştir.
Belirgin biventriküler hipertrofi gösteren son dönem hipertrofik kardiyomiyopati olgusu: Yeni ekokardiyografik yöntemlerle değerlendirme
Hypertrophic cardiomyopathy is the most common genetic cardiac disorder. This disease, which is the leading cause of sudden cardiac death in young patients, is typically characterized by idiopathic hypertrophy of the left and sometimes the right ventricle. We present a case of end-stage hypertrophic cardiomyopathy with impressive biventricular hypertrophy which was evaluated with novel echocardiographic modalities.
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- 1.Cheng T. Hypertrophic cardiomyopathy is a biventricular disease. Int J Cardiol 200816;129:3-4.
- 2.Maron MS, Hauser TH, Duborow E, Horst TA, Kissinger KV, Udelson JE et al. Right ventricular involvement in hypertrophic cardiomyopathy. Am J Cardiol 2007;100:1293-8.
- 3.Maron BJ, Piccininno M, Casey SA, Bernabò P, Spirito P. Relation of extreme left ventricular hypertrophy to age in hypertrophic cardiomyopathy. Am J Cardiol 20031;91:626-8.
- 4.Maron BJ. Hypertrophic cardiomyopathy: a systematic review. JAMA 2002;287:1308-20.
- 5.Olivotto I, Cecchi F, Gistri R, Lorenzoni R, Chiriatti G, Girolami F, et al. Relevance of coronary microvascular flow impairment to long-term remodeling and systolic dysfunction in hypertrophic cardiomyopathy. J Am Coll Cardiol 2006;47:1043-8.
- 6.Harris KM, Spirito P, Maron MS, Zenovich AG, Formisano F, Lesser JR, et al. Prevalence, clinical profile, and significance of left ventricular remodeling in the end-stage phase of hypertrophic cardiomyopathy. Circulation 2006;114:216-25.
- 7.Melacini P, Basso C, Angelini A, Calore C, Bobbo F, Tokajuk B, et al. Clinicopathological profiles of progressive heart failure in hypertrophic cardiomyopathy. Eur Heart J 2010;31:2111-23.
- 8.Spirito P, Bellone P, Harris KM, Bernabo P, Bruzzi P, Maron BJ. Magnitude of left ventricular hypertrophy and risk of sudden death in hypertrophic cardiomyopathy. N Engl J Med 2000;342:1778-85.
- 9.Nagueh SF, Bachinski LL, Meyer D, Hill R, Zoghbi WA, Tam JW, et al. Tissue Doppler imaging consistently detects myocardial abnormalities in patients with hypertrophic cardiomyopathy and provides a novel means for an early diagnosis before and independently of hypertrophy. Circulation 2001;104:128-30.
- 10.DAndrea A, Caso P, Severino S, Cuomo S, Capozzi G, Calabrò P, et al. Prognostic value of intra-left ventricular electromechanical asynchrony in patients with hypertrophic cardiomyopathy. Eur Heart J 2006;27:1311-8.
- 11.Serri K, Reant P, Lafitte M, Berhouet M, Le Bouffos V, Roudaut R, et al. Global and regional myocardial function quantification by two-dimensional strain: application in hypertrophic cardiomyopathy. J Am Coll Cardiol 2006;47:1175-81.
- 12.Popović ZB, Kwon DH, Mishra M, Buakhamsri A, Greenberg NL, Thamilarasan M, et al. Association between regional ventricular function and myocardial fibrosis in hypertrophic cardiomyopathy assessed by speckle tracking echocardiography and delayed hyper enhancement magnetic resonance imaging. J Am Soc Echocardiogr 2008;21:1299-305.
- 13. Sun JP, Stewart WJ, Yang XS, Donnell RO, Leon AR, Felner JM, et al. Differentiation of hypertrophic cardiomyopathy and cardiac amyloidosis from other causes of ventricular wall thickening by two-dimensional strain imaging echocardiography. Am J Cardiol 2009;103:411-5.
- 14. Chang SA, Kim HK, Kim DH, Kim JC, Kim YJ, Kim HC, et al. Left ventricular twist mechanics in patients with apical hypertrophic cardiomyopathy: assessment with 2D speckle tracking echocardiography. Heart 2010;96:49-55.
- 15. Abozguia K, Nallur-Shivu G, Phan TT, Ahmed I, Kalra R, Weaver RA, et al. Left ventricular strain and untwist in hypertrophic cardiomyopathy: relation to exercise capacity. Am Heart J 2010;159:825-32.
- 16. Salustri A, Kofflard MJ, Roelandt JR, Nosir Y, Trocino G, Keane D, et al. Assessment of left ventricular outflow in hypertrophic cardiomyopathy using anyplane and paraplane analysis of three-dimensional echocardiography. Am J Cardiol 1996;78:462-8.
- 17. Oe H, Hozumi T, Arai K, Matsumura Y, Negishi K, Sugioka K, et al. Comparison of accurate measurement of left ventricular mass in patients with hypertrophied hearts by real-time three-dimensional echocardiography versus magnetic resonance imaging. Am J Cardiol 2005;95:1263-7.
- 18. De Gregorio C, Recupero A, Grimaldi P, Coglitore S. Can transthoracic live 3-dimensional echocardiography improve the recognition of midventricular obliteration in hypertrophic obstructive cardiomyopathy? J Am Soc Echocardiogr 2006;19:1190.1-4.