Aynı Kitle İçerisinde Dermatofibrosarkom Protuberans Ve Miksofibrosarkom, Çok Nadir Olgu Sunumu

Biz aynı kitle içerisinde dermatofibrosarkom protuberans ve orta dereceli miksofibrosarkom birlikteliğinin izlendiği çok nadir bir kompozit tümör vakası sunmaktayız. Vakamız, 58 yaşında kadın hastaya ait, sağ göğüs altında yıllardır mevcut olan, son zamanlarda büyüme gösteren deri üzerinde protrüde kitledir. Makroskopik olarak yan yana olan her iki tümör bileşeninin de birbiri ile devamlılığı mevcut olup, subkutan dokuya kadar uzanmaktadır. İki tümör arasında mikroskobik olarak da belirgin bağlantı alanları görülmüştür. Dermatofibrosarkom protuberans vakalarında fibrosarkom transformasyonu yanı sıra nadiren pleomorfik sarkom transformasyonu gösteren olgularda bildirilmektedir. Bizim olgumuzda aynı tümör içerisinde iki ayrı tümörün izlenmesi dermatofibrosarkom protuberanslar vakalarının daha önce literatürde bildirilmemiş miksofibrosarkoma da dönüşebileceğini düşündürmektedir.

Anahtar Kelimeler:

Dermatofibrosarkom prıtuberans, miksofibrosarkom, mezenkimal tümör

Dermatofibrosarcoma Protuberans And Myxofibrosarcoma In The Same Mass, Very Rare Case Report

We present a very rare case of composite tumor consisting of dermatofibrosarcoma protuberans and intermediate grade myxofibrosarcoma with in the same mass. Our case is a protruded mass on the skin, which has been present for years under the right chest of a 58-year-old female patient, and has been growing recently. Both tumor components, which are adjacent to each other macroscopically, have continuity with each other and extend to the subcutaneous tissue. Microscopically, distinct connection areas were also observed between them. Besides known fibrosarcoma transformation of dermatofibrosarcoma protuberans, cases that are rarely transformed into pleomorphic sarcoma are known. However, in our case, the existing of two different tumors with in the same mass suggests that dermatofibrosarcoma protuberans may also transform into a myxofibrosarcoma, which has not been previously reported in the literature.

Keywords:

Dermatofibrosarcoma precuberance, myxofibrosarcoma, mesenchymal tumor,

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