Renal anjiyomiyolipomun ölümcül komplikasyonu olarak Wunderlich sendromu: olgu sunumu ve literatürün gözden geçirilmesi

Wunderlich sendromu (WS), subkapsüler ve perirenal boşluklara nonumumatik renal kanama ile ilişkili nadir bir akut karın hastalığıdır. Renal hücreli karsinom, anjiyomiyolipom, böbrek kistleri, vaskülit veya kan disprasileri bilinen risk faktörleri arasındadır. Masif retroperitoneal kanama ile ilişkili 59 yaşındaki bir kadın hastada Wunderlich sendromu olgusunu sunuyoruz.

Anahtar Kelimeler:

Wunderlich sendromu, anjiyomiyolipom, bilgisayarlı tomografi

Wunderlich's syndrome as the fatal complication of a renal angiomyolipoma: a case report and review of the literature

Wunderlich syndrome (WS) is a rare acute abdominal condition, which is characterized with spontaneous nontraumatic renal haemorrhage into the subcapsular and perirenal spaces. Renal cell carcinoma, angiomyolipoma, renal cysts, vasculitis or blood dyscrasias are among the known risk factors. We report a case of Wunderlich's syndrome in an 59 year old woman associated with massive retroperitoneal hemorrhage.

Keywords:

Wunderlich syndrome, angiomyolipoma, computed tomography,

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