Miğraci TOSUN, Burcu TORUMTAY ALIÇA, Erdal MALATYALIOĞLU, Mehmet ÇETİNKAYA, Arif KÖKÇÜ, Tayfun ALPER, Gönül OĞUR

İntakt Ventriküler Septumun Eşlik Ettiği Pulmoner Atrezi

İntakt ventriküler septumun eşlik ettiği pulmoner atrezi nadir görülen kardiyak bir malformasyondur. 10.000 canlı doğumda 0,58 oranında görülür. Ağır sağ kalp hipoplazisi olan vakalarının çoğunda prognoz kötü olduğundan erken tanı konması önemlidir. Pulmonary atresia with intact ventricular septum is a rare cardiac malformation which is present at live birth of 0.58 per 10,000. Because of the prognosis is poor in most severe right heart hypoplasia cases,early diagnosis is critical.Konjenital kalp anomalileri perinatal mortalitenin önde gelen nedenlerinden biridir. Canlı doğumların %0,6' sı ve ölü doğumların % 10' unda konjenital kalp anomalilerine rastlanmaktadır (Fröber ve ark., 2001).

Keywords:

Pulmoner Atrezi, İntakt Ventriküler Septum, Hipoplastik Sağ Kalp,

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