Suna SARIKAYA, Murat YILMAZ, Ersin Kasım ULUSOY, Gürdal ORHAN, Fikri AK, Tahir Kurtuluş YOLDAŞ

Nöbet ile Başvuran Moyamoya Hastalığı Olgu Sunumu

Moyamoya hastalığı intarakraniyal internal karotis arterlerin idiapotik steno-oklüzyonu ve anormal vasküler ağlar ile karakterizedir. Bu vaka sunumunda acil servise nöbet geçirme şikayeti ile başvuran otuz dört yaşındaki erkek hastaya, anamnez, muayene bilgisayarlı beyin tomografisi (BBT) ve dijital substraksiyon anjiyografi (DSA) ile Moyamoya hastalığı tanısı konuldu. Bu vaka ilk olarak nöbet ile başvurması ve nadir görülmesi nedeniyle sunuldu.

Anahtar Kelimeler:

Moyamoya hastalığı, inme, nöbet

A Case Report of Moyamoya Disease Presenting with Seizure

Moyamoya disease is characterised by idiopathic steno-occlusion at the intracranial carotid arteries with concomitant abnormal vascular networks. In this case report, a 34 year old man presented to the emergency room with a complaint of seizure and was diagnosed with Moyamoya disease by history, examination, cranial computed tomography (CCT) and digital subtraction angiography (DSA). This case was reported as it is the first known example of a patient presenting initially with seizure, as well as the rarity of the disease

Keywords:

Moyamoya disease, stroke, seizure,

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Yamamoto, M, Aoyagi M, Tijima S. İncrease in elastin gene expresion and protein synthesis in arterial smooth muscle cell derived from pa- tients with moyamoya disease. Stroke 1998; 28: 1733-8. [Crossref]
Suzuki J, Kodowa N. Moyamoya disease. Stroke 1983; 14: 104-9. [Crossref]
Pavlakis SG, Verlander PC, Gould RJ, Strimling BC, Auerbach AD. Fanconi anemia and moyamoya: Evidencefor an association. Neurology 1995; 45: 998-1000. [Crossref]
Menkes JH. Cerebrovascular disorders. In Menkes JH editor. Textbook of child neurology. 5.th edit. Baltimore,Williams and Willkins. 1995.pp.702-24.
Masuda J, Ogata J, Yamaguchi T. Moyamoya disease. In: Barnett HJM, Mohr JP, Stein BM, Yatsu FM, ed. Stroke: Pathophysiology, diagnosis, and management, ed 3. New York: Churchill Livingstone; 1998: 815.
Karasawa J, Touho H, Ohnishi H, Miyamoto S, Kikuchi H. Cerebral revas- cularization using omental transplantation for childhood moyamoya disease. J Neurosurg 1993; 79: 192-6. [Crossref]
Kohno K, Oka Y, Kohno S, Ohta S, Kumon Y, Sakaki S. Cerebral blood flow measurements as an indicator for an indirect revascularization proce- dure for adult patients with moyamoya disease. Neurosurgery 1998; 42: 752-8. [Crossref]
Yang S, Yu JL, Wang HL, Wang B, Luo Q. Endovascular embolization of distal anterior choroidal artery aneurysms associated with moyamoya disease. A report of two cases and a literature review. Interv Neuroradiol 2010; 16: 433-41.