Fatma MUTLU SARIGUZEL, Bilal AYGUN, Cigdem KARAKUKCU, Derya KOCER, Ahmet GODEKMERDAN

Yaygın Değişken İmmun Yetmezlikli Bir Olguda Behçet Hastalığı

Yaygın değişken immun yetmezlik, yaygın yetersiz antikor yanıtı ile karakterize bir hastalıktır ve bu olguların yaklaşık %20’sinde otoimmün bir hastalık gelişebilir. Behçet hastalığı, ağızda ve genital bölgede tekrar eden ülserlerlerin birlikte bulunmasıyla teşhis edilen nadir bir vaskülittir. Behçet hastalığında gastrointestinal tutulum olabilir. Behçet hastalığı ve yaygın değişken immun yetmezlik hastalığının eşzamanlı birlikte seyreden bir olguyu sunmayı amaçladık.

Anahtar Kelimeler:

Yaygın değişken immun yetmezlik, Behçet hastalığı, otoimmunite, gastrointestinal tutulum.

Behcet’s disease in a patient with common variable immunodeficiency

Common variable immunodeficiency (CVID) is one of the most common antibody deficiencies and about 20% of patients with CVID develop an autoimmune complication. Behçet's disease (BD) is a rare vasculitis diagnosed by the presence of recurrent oral and genital ulcers. Gastrointestinal involvement in Behçet's disease may be. Here, we report an uncommon case where a patient suffered from BD and CVID, together.

Keywords:

Common variable immunodeficiency, Behcet’s disease, autoimmunity, gastrointestinal involvement.,

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